| P50 | author | José Antonio Enríquez | Q40627615 |
| P2093 | author name string | Giorgio Lenaz | |
| P2860 | cites work | NDUFA4 is a subunit of complex IV of the mammalian electron transport chain | Q24296926 |
| | Mitochondrial respiratory chain supercomplexes are destabilized in Barth Syndrome patients | Q24297605 |
| | Phosphoproteome analysis of functional mitochondria isolated from resting human muscle reveals extensive phosphorylation of inner membrane protein complexes and enzymes | Q24299408 |
| | Dysfunctions of cellular oxidative metabolism in patients with mutations in the NDUFS1 and NDUFS4 genes of complex I | Q24304454 |
| | Respiratory complex III is required to maintain complex I in mammalian mitochondria | Q24322645 |
| | Supercomplexes in the respiratory chains of yeast and mammalian mitochondria | Q24599994 |
| | Making heads or tails of phospholipids in mitochondria | Q24601121 |
| | Evidence for Physical Association of Mitochondrial Fatty Acid Oxidation and Oxidative Phosphorylation Complexes | Q24604387 |
| | Oxidative stress, mitochondrial dysfunction, and aging | Q24635310 |
| | Specific roles of protein-phospholipid interactions in the yeast cytochrome bc1 complex structure | Q27636481 |
| | Arrangement of electron transport chain components in bovine mitochondrial supercomplex I1III2IV1 | Q27673724 |
| | Identification of a protein mediating respiratory supercomplex stability | Q27932303 |
| | Rcf1 and Rcf2, members of the hypoxia-induced gene 1 protein family, are critical components of the mitochondrial cytochrome bc1-cytochrome c oxidase supercomplex | Q27932423 |
| | Barth syndrome may be due to an acyltransferase deficiency | Q27936025 |
| | Taz1, an outer mitochondrial membrane protein, affects stability and assembly of inner membrane protein complexes: implications for Barth Syndrome | Q27936928 |
| | Rcf1 mediates cytochrome oxidase assembly and respirasome formation, revealing heterogeneity of the enzyme complex | Q27937145 |
| | Atp10p assists assembly of Atp6p into the F0 unit of the yeast mitochondrial ATPase | Q27939966 |
| | The complexity of cardiolipin in health and disease | Q28395624 |
| | Beneficial effects of a Q-ter based nutritional mixture on functional performance, mitochondrial function, and oxidative stress in rats | Q28473890 |
| | A water soluble CoQ10 formulation improves intracellular distribution and promotes mitochondrial respiration in cultured cells | Q28481504 |
| | A phosphodiesterase 2A isoform localized to mitochondria regulates respiration | Q28506723 |
| | Mice lacking COX10 in skeletal muscle recapitulate the phenotype of progressive mitochondrial myopathies associated with cytochrome c oxidase deficiency | Q28512560 |
| | Control of oxygen free radical formation from mitochondrial complex I: roles for protein kinase A and pyruvate dehydrogenase kinase | Q28582573 |
| | Cytochrome c oxidase is required for the assembly/stability of respiratory complex I in mouse fibroblasts | Q28585444 |
| | Supercomplex assembly determines electron flux in the mitochondrial electron transport chain | Q28590886 |
| | Cardiolipin stabilizes respiratory chain supercomplexes | Q29615470 |
| | A defect in the mitochondrial complex III, but not complex IV, triggers early ROS-dependent damage in defined brain regions. | Q30416049 |
| | Membrane deformation under local pH gradient: mimicking mitochondrial cristae dynamics | Q30484410 |
| | Mitochondrial membrane potential in human neutrophils is maintained by complex III activity in the absence of supercomplex organisation | Q33330306 |
| | Direct demonstration of half-of-the-sites reactivity in the dimeric cytochrome bc1 complex: enzyme with one inactive monomer is fully active but unable to activate the second ubiquinol oxidation site in response to ligand binding at the ubiquinone r | Q33581364 |
| | Mutations in mitochondrial complex III uniquely affect complex I in Caenorhabditis elegans | Q41197782 |
| | Loss of tafazzin in yeast leads to increased oxidative stress during respiratory growth | Q41577989 |
| | Ubiquinone reduction pattern in pigeon heart mitochondria. Identification of three distinct ubiquinone pools | Q41898251 |
| | Complex I function is defective in complex IV-deficient Caenorhabditis elegans | Q41983183 |
| | Phosphorylation and kinetics of mammalian cytochrome c oxidase | Q42169014 |
| | Phosphatidylethanolamine and cardiolipin differentially affect the stability of mitochondrial respiratory chain supercomplexes | Q42406378 |
| | Reactive oxygen species affect mitochondrial electron transport complex I activity through oxidative cardiolipin damage | Q42519929 |
| | Antioxidant treatment of patients with Friedreich ataxia: four-year follow-up | Q42653222 |
| | Mitochondrial respiratory supercomplex association limits production of reactive oxygen species from complex I. | Q42678131 |
| | Regulation by the cAMP cascade of oxygen free radical balance in mammalian cells. | Q42802469 |
| | The three-dimensional structure of complex I from Yarrowia lipolytica: a highly dynamic enzyme | Q43024932 |
| | Cyclic AMP produced inside mitochondria regulates oxidative phosphorylation | Q43124399 |
| | Lack of cytochrome c in mouse fibroblasts disrupts assembly/stability of respiratory complexes I and IV. | Q43182550 |
| | Mitochondrial Complex I decrease is responsible for bioenergetic dysfunction in K-ras transformed cells | Q43237277 |
| | Saturation kinetics of coenzyme Q in NADH and succinate oxidation in beef heart mitochondria | Q43646998 |
| | A novel nonsense mutation (Q352X) in the mitochondrial cytochrome b gene associated with a combined deficiency of complexes I and III. | Q43814295 |
| | Decreased complex III activity in mitochondria isolated from rat heart subjected to ischemia and reperfusion: role of reactive oxygen species and cardiolipin | Q44315294 |
| | Coenzyme Q10 reduces beta-amyloid plaque in an APP/PS1 transgenic mouse model of Alzheimer's disease | Q44495822 |
| | Progressive exercise intolerance associated with a new muscle-restricted nonsense mutation (G142X) in the mitochondrial cytochrome b gene | Q44594516 |
| | The mitochondrial and prokaryotic proton-translocating NADH:ubiquinone oxidoreductases: similarities and dissimilarities of the quinone-junction sites. | Q44689778 |
| | Regulation of NADH/CoQ oxidoreductase: do phosphorylation events affect activity? | Q44871296 |
| | The mitochondrial respiratory chain is partially organized in a supercomplex assembly: kinetic evidence using flux control analysis | Q44942853 |
| | cAMP-dependent protein kinase regulates the mitochondrial import of the nuclear encoded NDUFS4 subunit of complex I. | Q46740409 |
| | Functional dynamic compartmentalization of respiratory chain intermediate substrates: implications for the control of energy production and mitochondrial diseases. | Q46799359 |
| | Significance of respirasomes for the assembly/stability of human respiratory chain complex I. | Q47316196 |
| | Metabolic control analysis of cellular respiration in situ in intraoperational samples of human breast cancer | Q47335770 |
| | Ageing alters the supramolecular architecture of OxPhos complexes in rat brain cortex | Q48305782 |
| | Species- and tissue-specific relationships between mitochondrial permeability transition and generation of ROS in brain and liver mitochondria of rats and mice. | Q48392931 |
| | Studies on the mechanims of oxidative phosphorylation. IX. Effect of cytochrome c on energy-linked processes | Q50336021 |
| | ROS generation and multiple forms of mammalian mitochondrial glycerol-3-phosphate dehydrogenase. | Q50486651 |
| | The kinetics of the redox reactions of ubiquinone related to the electron-transport activity in the respiratory chain. | Q52473651 |
| | Soluble cytochrome b-c1 complex and the reconstitution of succinate-cytochrome c reductase. | Q53758544 |
| | Mechanism of superoxide and hydrogen peroxide generation by human electron-transfer flavoprotein and pathological variants. | Q55056121 |
| | Metabolic channelling and control of the flux | Q56689817 |
| | Steady-state kinetics of the overall oxidative phosphorylation reaction in heart mitochondria. Determination of the coupling relationships between the respiratory reactions and miscellaneous observations concerning rate-limiting steps | Q72415463 |
| | Cardiolipin requirement for electron transfer in complex I and III of the mitochondrial respiratory chain | Q72879330 |
| | Energized cation transport by complex III (ubiquinone-cytochrome C reductase) | Q72881622 |
| | Lateral diffusion of ubiquinone during electron transfer in phospholipid- and ubiquinone-enriched mitochondrial membranes | Q72940609 |
| | Phospholipase A(2) digestion of cardiolipin bound to bovine cytochrome c oxidase alters both activity and quaternary structure | Q73168063 |
| | A deficiency in respiratory complex I in heart mitochondria from vitamin A-deficient rats is counteracted by an increase in coenzyme Q | Q73326211 |
| | Direct evidence for increased hydroxyl radicals originating from superoxide in the failing myocardium | Q73427285 |
| | The effect of reactive oxygen species generated from the mitochondrial electron transport chain on the cytochrome c oxidase activity and on the cardiolipin content in bovine heart submitochondrial particles | Q73465535 |
| | Coenzyme Q10 reverses pathological phenotype and reduces apoptosis in familial CoQ10 deficiency | Q74365016 |
| | Electron transport-linked ubiquinone-dependent recycling of alpha-tocopherol inhibits autooxidation of mitochondrial membranes | Q74547741 |
| | Generation of superoxide anion by succinate-cytochrome c reductase from bovine heart mitochondria | Q77677718 |
| | Comparisons of coenzyme Q bound to mitochondrial membrane proteins among different mammalian species | Q78115676 |
| | Respiratory complexes III and IV are not essential for the assembly/stability of complex I in fungi | Q83102320 |
| | Cardiac mitochondria in heart failure: normal cardiolipin profile and increased threonine phosphorylation of complex IV | Q83409915 |
| | Modulation of sulfide oxidation and toxicity in rat mitochondria by dehydroascorbic acid | Q84432343 |
| | Lipid packing variations induced by pH in cardiolipin-containing bilayers: the driving force for the cristae-like shape instability | Q84624577 |
| | Coenzyme Q10; an adjunctive therapy for congestive heart failure? | Q84992866 |
| | Mitochondrial complex III stabilizes complex I in the absence of NDUFS4 to provide partial activity | Q85030067 |
| | Modulation of mitochondrial protein phosphorylation by soluble adenylyl cyclase ameliorates cytochrome oxidase defects | Q33623775 |
| | Respiratory Chain Complexes in Dynamic Mitochondria Display a Patchy Distribution in Life Cells | Q33650944 |
| | Localization and mobility of coenzyme Q in lipid bilayers and membranes | Q33693125 |
| | Age-related decline in mitochondrial bioenergetics: does supercomplex destabilization determine lower oxidative capacity and higher superoxide production? | Q33897468 |
| | Quinone-responsive multiple respiratory-chain dysfunction due to widespread coenzyme Q10 deficiency | Q33916496 |
| | Structure of a mitochondrial supercomplex formed by respiratory-chain complexes I and III | Q33927498 |
| | The ratio of oxidative phosphorylation complexes I-V in bovine heart mitochondria and the composition of respiratory chain supercomplexes | Q33953875 |
| | A critical appraisal of the mitochondrial coenzyme Q pool | Q33956376 |
| | Gluing the respiratory chain together. Cardiolipin is required for supercomplex formation in the inner mitochondrial membrane | Q33961781 |
| | Architecture of active mammalian respiratory chain supercomplexes. | Q33994333 |
| | Three-dimensional structure of the respiratory chain supercomplex I1III2IV1 from bovine heart mitochondria. | Q34007450 |
| | Role of phospholipids in respiratory cytochrome bc(1) complex catalysis and supercomplex formation | Q34016363 |
| | Interaction of complexes I, III, and IV within the bovine respirasome by single particle cryoelectron tomography | Q34028316 |
| | Supramolecular organisation of the mitochondrial respiratory chain: a new challenge for the mechanism and control of oxidative phosphorylation | Q34032506 |
| | The respiratory chain in yeast behaves as a single functional unit | Q34066006 |
| | Studies on the electron transfer system. XLII. Reconstitution of the electron transfer system. | Q34252417 |
| | Studies on the electron transfer system. XL. Preparation and properties of mitochondrial DPNH-coenzyme Q reductase. | Q34252424 |
| | HIG1, a novel regulator of mitochondrial γ-secretase, maintains normal mitochondrial function | Q34256113 |
| | Nonbilayer lipids affect peripheral and integral membrane proteins via changes in the lateral pressure profile. | Q34363960 |
| | Coenzyme Q10 therapy before cardiac surgery improves mitochondrial function and in vitro contractility of myocardial tissue | Q34381788 |
| | Role of uncoupled and non-coupled oxidations in maintenance of safely low levels of oxygen and its one-electron reductants | Q34402690 |
| | Steady-state kinetics of reduction of coenzyme Q analogs by glycerol-3-phosphate dehydrogenase in brown adipose tissue mitochondria | Q34434365 |
| | Phosphoproteome analysis reveals regulatory sites in major pathways of cardiac mitochondria | Q34551789 |
| | Natural distribution and occurrence of coenzyme Q homologues | Q34627222 |
| | The mitochondrial electron transfer chain | Q34697908 |
| | Questioning the functional relevance of mitochondrial supercomplexes by time-resolved analysis of the respiratory chain | Q35546896 |
| | The composition of plant mitochondrial supercomplexes changes with oxygen availability. | Q35604504 |
| | Structural and functional organization of Complex I in the mitochondrial respiratory chain | Q35616438 |
| | Cells lacking Rieske iron-sulfur protein have a reactive oxygen species-associated decrease in respiratory complexes I and IV. | Q35665686 |
| | Mitochondrial complex I plays an essential role in human respirasome assembly | Q35868845 |
| | Two protein kinase C isoforms, δ and ε, regulate energy homeostasis in mitochondria by transmitting opposing signals to the pyruvate dehydrogenase complex | Q36117484 |
| | Coenzyme Q10 administration increases brain mitochondrial concentrations and exerts neuroprotective effects | Q36225925 |
| | A quantitative map of the liver mitochondrial phosphoproteome reveals posttranslational control of ketogenesis | Q36423097 |
| | Kinetics of integrated electron transfer in the mitochondrial respiratory chain: random collisions vs. solid state electron channeling | Q36621081 |
| | Physiological significance of metabolic channelling | Q36835187 |
| | Cardiolipin defines the interactome of the major ADP/ATP carrier protein of the mitochondrial inner membrane | Q36860381 |
| | Cardiac mitochondria in heart failure: decrease in respirasomes and oxidative phosphorylation | Q36870637 |
| | Restoration of electron transport without proton pumping in mammalian mitochondria. | Q36977872 |
| | Is supercomplex organization of the respiratory chain required for optimal electron transfer activity? | Q37153827 |
| | Features and applications of blue-native and clear-native electrophoresis | Q37258525 |
| | Supercomplexes of the mitochondrial electron transport chain decline in the aging rat heart. | Q37388302 |
| | Redox sensitive signaling pathways in cardiac remodeling, hypertrophy and failure | Q37410415 |
| | From protons to OXPHOS supercomplexes and Alzheimer's disease: structure-dynamics-function relationships of energy-transducing membranes | Q37413516 |
| | Control of respiration by cytochrome c oxidase in intact cells: role of the membrane potential | Q37431935 |
| | New aspects of impaired mitochondrial function in heart failure | Q37434049 |
| | Structure and organization of mitochondrial respiratory complexes: a new understanding of an old subject | Q37594110 |
| | Mitochondrial respiratory chain super-complex I-III in physiology and pathology | Q37684148 |
| | Oxidative stress, mitochondrial bioenergetics, and cardiolipin in aging | Q37696660 |
| | Coenzyme Q and mitochondrial disease | Q37785517 |
| | Bioavailability enhancement of coenzyme Q10: an extensive review of patents. | Q37791565 |
| | Mitochondrial thiols in antioxidant protection and redox signaling: distinct roles for glutathionylation and other thiol modifications | Q37939954 |
| | New developments on the functions of coenzyme Q in mitochondria | Q37944537 |
| | Src kinases are important regulators of mitochondrial functions | Q38040973 |
| | Evolving concepts of oxidative stress and reactive oxygen species in cardiovascular disease. | Q38041505 |
| | The mitochondrial protein import machinery has multiple connections to the respiratory chain | Q38070291 |
| | cAMP-dependent tyrosine phosphorylation of subunit I inhibits cytochrome c oxidase activity | Q39373761 |
| | Supramolecular organizations in the aerobic respiratory chain of Escherichia coli | Q39480857 |
| | The random collision model and a critical assessment of diffusion and collision in mitochondrial electron transport | Q39505283 |
| | Protein phosphorylation and prevention of cytochrome oxidase inhibition by ATP: coupled mechanisms of energy metabolism regulation | Q39530676 |
| | Variation of flux control coefficient of cytochrome c oxidase and of the other respiratory chain complexes at different values of protonmotive force occurs by a threshold mechanism. | Q39544308 |
| | Respiratory active mitochondrial supercomplexes. | Q39913363 |
| | Subunits of mitochondrial complex I exist as part of matrix- and membrane-associated subcomplexes in living cells | Q39934113 |
| | Mammalian complex I: a regulable and vulnerable pacemaker in mitochondrial respiratory function | Q39985545 |
| | The interaction between mitochondrial NADH-ubiquinone oxidoreductase and ubiquinol-cytochrome c oxidoreductase. Evidence for stoicheiometric association | Q40195668 |
| | The interaction between mitochondrial NADH-ubiquinone oxidoreductase and ubiquinol-cytochrome c oxidoreductase. Restoration of ubiquinone-pool behaviour | Q40195673 |
| | Nuclear magnetic resonance investigation of the cytochrome oxidase-phospholipid interaction: a new model for boundary lipid | Q40243491 |
| | Respiratory chain supercomplexes set the threshold for respiration defects in human mtDNA mutant cybrids | Q40272913 |
| | Control by cytochrome c oxidase of the cellular oxidative phosphorylation system depends on the mitochondrial energy state | Q40305746 |
| P433 | issue | 3-4 | |
| P407 | language of work or name | English | Q1860 |
| P304 | page(s) | 119-140 | |
| P577 | publication date | 2014-07-01 | |
| P1433 | published in | Molecular syndromology | Q26842514 |
| P1476 | title | Coenzyme q and the respiratory chain: coenzyme q pool and mitochondrial supercomplexes | |
| P478 | volume | 5 | |