scholarly article | Q13442814 |
P50 | author | Joaquín Arenas | Q56939581 |
P2093 | author name string | Cristina Ugalde | |
Antoni Barrientos | |||
David Moreno-Lastres | |||
Flavia Fontanesi | |||
Inés García-Consuegra | |||
Miguel A Martín | |||
P2860 | cites work | NDUFS6 mutations are a novel cause of lethal neonatal mitochondrial complex I deficiency | Q24304313 |
Differences in assembly or stability of complex I and other mitochondrial OXPHOS complexes in inherited complex I deficiency | Q24306549 | ||
Respiratory complex III is required to maintain complex I in mammalian mitochondria | Q24322645 | ||
Mutation of C20orf7 disrupts complex I assembly and causes lethal neonatal mitochondrial disease | Q24336408 | ||
Identification of mitochondrial complex I assembly intermediates by tracing tagged NDUFS3 demonstrates the entry point of mitochondrial subunits | Q24338844 | ||
A molecular chaperone for mitochondrial complex I assembly is mutated in a progressive encephalopathy | Q24536088 | ||
Multiprotein complex containing succinate dehydrogenase confers mitochondrial ATP-sensitive K+ channel activity | Q24563970 | ||
Supercomplexes in the respiratory chains of yeast and mammalian mitochondria | Q24599994 | ||
Analysis of the assembly profiles for mitochondrial- and nuclear-DNA-encoded subunits into complex I | Q24683107 | ||
Arrangement of electron transport chain components in bovine mitochondrial supercomplex I1III2IV1 | Q27673724 | ||
Assembly of cytochrome-c oxidase in cultured human cells | Q28276105 | ||
Cytochrome c oxidase is required for the assembly/stability of respiratory complex I in mouse fibroblasts | Q28585444 | ||
Human cells lacking mtDNA: repopulation with exogenous mitochondria by complementation | Q29614475 | ||
Respiratory Chain Complexes in Dynamic Mitochondria Display a Patchy Distribution in Life Cells | Q33650944 | ||
The ratio of oxidative phosphorylation complexes I-V in bovine heart mitochondria and the composition of respiratory chain supercomplexes | Q33953875 | ||
Architecture of active mammalian respiratory chain supercomplexes. | Q33994333 | ||
A structural model of the cytochrome C reductase/oxidase supercomplex from yeast mitochondria | Q34002630 | ||
Interaction of complexes I, III, and IV within the bovine respirasome by single particle cryoelectron tomography | Q34028316 | ||
Investigation of the complex I assembly chaperones B17.2L and NDUFAF1 in a cohort of CI deficient patients | Q34612081 | ||
Impaired complex III assembly associated with BCS1L gene mutations in isolated mitochondrial encephalopathy | Q34614921 | ||
Blue Native electrophoresis to study mitochondrial and other protein complexes | Q34675865 | ||
Biogenesis of the yeast cytochrome bc1 complex. | Q37172145 | ||
Assembly of the oxidative phosphorylation system in humans: what we have learned by studying its defects | Q37213554 | ||
Supramolecular organization of ATP synthase and respiratory chain in mitochondrial membranes | Q37376950 | ||
Synthesis of cytochrome c oxidase subunit 1 is translationally downregulated in the absence of functional F1F0-ATP synthase | Q37394160 | ||
Structure and organization of mitochondrial respiratory complexes: a new understanding of an old subject | Q37594110 | ||
Assembly factors of human mitochondrial complex I and their defects in disease | Q37765531 | ||
Supramolecular organizations in the aerobic respiratory chain of Escherichia coli | Q39480857 | ||
The random collision model and a critical assessment of diffusion and collision in mitochondrial electron transport | Q39505283 | ||
Variation of flux control coefficient of cytochrome c oxidase and of the other respiratory chain complexes at different values of protonmotive force occurs by a threshold mechanism. | Q39544308 | ||
Respiratory active mitochondrial supercomplexes. | Q39913363 | ||
Mitochondrial DNA background modulates the assembly kinetics of OXPHOS complexes in a cellular model of mitochondrial disease. | Q39937507 | ||
An assembled complex IV maintains the stability and activity of complex I in mammalian mitochondria | Q40142379 | ||
Respiratory chain supercomplexes set the threshold for respiration defects in human mtDNA mutant cybrids | Q40272913 | ||
Cellular pathophysiological consequences of BCS1L mutations in mitochondrial complex III enzyme deficiency. | Q43047012 | ||
A novel nonsense mutation (Q352X) in the mitochondrial cytochrome b gene associated with a combined deficiency of complexes I and III. | Q43814295 | ||
Identification and characterization of a common set of complex I assembly intermediates in mitochondria from patients with complex I deficiency | Q44588150 | ||
Significance of respirasomes for the assembly/stability of human respiratory chain complex I. | Q47316196 | ||
Novel mutations in the NDUFS1 gene cause low residual activities in human complex I deficiencies | Q48240631 | ||
Human mitochondrial complex I assembles through the combination of evolutionary conserved modules: a framework to interpret complex I deficiencies. | Q50488580 | ||
Combined OXPHOS complex I and IV defect, due to mutated complex I assembly factor C20ORF7 | Q56592348 | ||
Novel insights into the assembly and function of human nuclear-encoded cytochromecoxidase subunits 4, 5a, 6a, 7a and 7b | Q57847623 | ||
A Simple and Rapid Assay of Oxidative Phosphorylation | Q59068452 | ||
Assembly of nuclear DNA-encoded subunits into mitochondrial complex IV, and their preferential integration into supercomplex forms in patient mitochondria | Q63359727 | ||
Combined enzymatic complex I and III deficiency associated with mutations in the nuclear encoded NDUFS4 gene | Q74177562 | ||
Early-onset multisystem mitochondrial disorder caused by a nonsense mutation in the mitochondrial DNA cytochrome C oxidase II gene | Q74518028 | ||
Mitochondrial complex III stabilizes complex I in the absence of NDUFS4 to provide partial activity | Q85030067 | ||
P433 | issue | 3 | |
P304 | page(s) | 324-335 | |
P577 | publication date | 2012-02-16 | |
P1433 | published in | Cell Metabolism | Q1254684 |
P1476 | title | Mitochondrial complex I plays an essential role in human respirasome assembly | |
P478 | volume | 15 |
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