| review article | Q7318358 |
| scholarly article | Q13442814 |
| P50 | author | Philine Wangemann | Q124360509 |
| P2860 | cites work | Mutations in the gene encoding B1 subunit of H+-ATPase cause renal tubular acidosis with sensorineural deafness | Q22008703 |
| Pendred syndrome is caused by mutations in a putative sulphate transporter gene (PDS) | Q24313229 | ||
| Novel ATP6V1B1 and ATP6V0A4 mutations in autosomal recessive distal renal tubular acidosis with new evidence for hearing loss | Q24315649 | ||
| Loss of KCNJ10 protein expression abolishes endocochlear potential and causes deafness in Pendred syndrome mouse model | Q24805411 | ||
| Apical membrane P2Y4 purinergic receptor controls K+ secretion by strial marginal cell epithelium | Q24814254 | ||
| Deafness and imbalance associated with inactivation of the secretory Na-K-2Cl co-transporter | Q28137646 | ||
| Gap junction systems in the mammalian cochlea | Q28141007 | ||
| Enlarged vestibular aqueduct: a radiological marker of pendred syndrome, and mutation of the PDS gene | Q28145781 | ||
| K+ cycling and the endocochlear potential | Q28198160 | ||
| Mutation of BSND causes Bartter syndrome with sensorineural deafness and kidney failure | Q28203023 | ||
| Barttin is a Cl- channel beta-subunit crucial for renal Cl- reabsorption and inner ear K+ secretion | Q28209314 | ||
| Connexin30 (Gjb6)-deficiency causes severe hearing impairment and lack of endocochlear potential | Q28218302 | ||
| Salt wasting and deafness resulting from mutations in two chloride channels | Q28252859 | ||
| KCNE1 mutations cause jervell and Lange-Nielsen syndrome | Q28253362 | ||
| Ion transport in guinea pig cochlea. I. Potassium and sodium transport | Q28275996 | ||
| Mutations in a plasma membrane Ca2+-ATPase gene cause deafness in deafwaddler mice | Q28279035 | ||
| Potassium secretion by nonsensory region of gerbil utricle in vitro. | Q54399127 | ||
| Presbycusis | Q56475342 | ||
| K+-induced swelling of vestibular dark cells is dependent on Na+ and Cl? and inhibited by piretanide | Q67666679 | ||
| Differentiation of inner ear fibrocytes according to their ion transport related activity | Q68270459 | ||
| Changes in Ca++ activity and DC potential in experimentally induced endolymphatic hydrops | Q68965276 | ||
| Mondini cochlea in Pendred's syndrome. A histological study | Q69653240 | ||
| Stimulus-related potassium changes in the organ of Corti of guinea-pig | Q69725468 | ||
| Electrochemical heterogeneity of the cochlear endolymph: effect of acetazolamide | Q71267936 | ||
| Enzyme-histochemical localization of carbonic anhydrase in the inner ear of the guinea pig and several improvements of the technique | Q71766066 | ||
| K(+)-induced stimulation of K+ secretion involves activation of the IsK channel in vestibular dark cells | Q71787208 | ||
| Glutamine synthetase and glutamate metabolism in the guinea pig cochlea | Q71850920 | ||
| Slowly activating voltage-dependent K+ conductance is apical pathway for K+ secretion in vestibular dark cells | Q72761805 | ||
| Immunological identification of an inward rectifier K+ channel (Kir4.1) in the intermediate cell (melanocyte) of the cochlear stria vascularis of gerbils and rats | Q73167219 | ||
| Plasmalemmal ATPase calcium pump localizes to inner and outer hair bundles | Q73503472 | ||
| Connexins 26 and 30 are co-assembled to form gap junctions in the cochlea of mice | Q73668171 | ||
| K+ secretion in strial marginal cells is stimulated via beta 1-adrenergic receptors but not via beta 2-adrenergic or vasopressin receptors | Q73838521 | ||
| cAMP increases K+ secretion via activation of apical IsK/KvLQT1 channels in strial marginal cells | Q74110716 | ||
| Calcium permeation of the turtle hair cell mechanotransducer channel and its relation to the composition of endolymph | Q74240502 | ||
| Expression of ATP-gated ion channels by Reissner's membrane epithelial cells | Q77168690 | ||
| Expression of the gap-junction connexins 26 and 30 in the rat cochlea | Q28287580 | ||
| The role of oxidative stress in noise-induced hearing loss | Q28294629 | ||
| Gap junctions in the rat cochlea: immunohistochemical and ultrastructural analysis | Q28300307 | ||
| The B1-subunit of the H(+) ATPase is required for maximal urinary acidification | Q28505674 | ||
| Blindness and auditory impairment caused by loss of the sodium bicarbonate cotransporter NBC3 | Q28511021 | ||
| Connexin29 is highly expressed in cochlear Schwann cells, and it is required for the normal development and function of the auditory nerve of mice | Q28511260 | ||
| Targeted disruption of the Kvlqt1 gene causes deafness and gastric hyperplasia in mice | Q28585784 | ||
| Mice lacking the B1 subunit of H+ -ATPase have normal hearing | Q28594705 | ||
| Gap junctional hemichannel-mediated ATP release and hearing controls in the inner ear | Q30476549 | ||
| Low endolymph calcium concentrations in deafwaddler2J mice suggest that PMCA2 contributes to endolymph calcium maintenance | Q30492656 | ||
| Purinergic modulation of cochlear partition resistance and its effect on the endocochlear potential in the Guinea pig. | Q30492676 | ||
| Targeted disruption of the Kcnq1 gene produces a mouse model of Jervell and Lange-Nielsen Syndrome. | Q30497826 | ||
| Fine structure of the intracochlear potential field. I. The silent current | Q30538771 | ||
| Targeted ablation of connexin26 in the inner ear epithelial gap junction network causes hearing impairment and cell death | Q30578611 | ||
| Immunolocalization of ClC-K chloride channel in strial marginal cells and vestibular dark cells | Q30731318 | ||
| Dye-coupling of melanocytes with endothelial cells and pericytes in the cochlea of gerbils | Q32054738 | ||
| Pathology of the Ear in the Cardio-Auditory Syndrome of Jervell and Lange-Nielsen (Recessive Deafness with Electrocardiographic Abnormalities) | Q33171482 | ||
| A new spontaneous mouse mutation in the Kcne1 gene | Q33823844 | ||
| Prevalence and evolutionary origins of the del(GJB6-D13S1830) mutation in the DFNB1 locus in hearing-impaired subjects: a multicenter study | Q33905363 | ||
| Gap junction-mediated intercellular biochemical coupling in cochlear supporting cells is required for normal cochlear functions | Q34084948 | ||
| Mechanisms of endocochlear potential generation by stria vascularis | Q34185692 | ||
| Distribution of immunoreactive alpha- and beta-subunit isoforms of Na,K-ATPase in the gerbil inner ear. | Q34329015 | ||
| Inner ear defects induced by null mutation of the isk gene | Q34412325 | ||
| Connexin26 is responsible for anionic molecule permeability in the cochlea for intercellular signalling and metabolic communications | Q34415753 | ||
| Immunohistochemical localization of the Na-K-Cl co-transporter (NKCC1) in the gerbil inner ear. | Q34430390 | ||
| Molecular genetics of hearing loss | Q34432273 | ||
| Regulation of endolymphatic fluid volume | Q34440903 | ||
| Mechano-electrical transduction currents in isolated vestibular hair cells of the chick | Q34469243 | ||
| I(sK) Channel in Strial Marginal Cells. Voltage-Dependence, Ion-Selectivity, Inhibition by 293B and Sensitivity to Clofilium. | Q35947685 | ||
| Localization of beta1-adrenergic receptors in the cochlea and the vestibular labyrinth | Q36063066 | ||
| Two mechanisms for transducer adaptation in vertebrate hair cells. | Q36209807 | ||
| Ototoxicity: therapeutic opportunities | Q36281577 | ||
| Mechanism generating endocochlear potential: role played by intermediate cells in stria vascularis | Q40173673 | ||
| Expression and functional phenotype of mouse ERG K+ channels in the inner ear: potential role in K+ regulation in the inner ear. | Q40370415 | ||
| Cochlear gap junctions coassembled from Cx26 and 30 show faster intercellular Ca2+ signaling than homomeric counterparts. | Q40461910 | ||
| Expression of connexin 26 and Na,K-ATPase in the developing mouse cochlear lateral wall: functional implications | Q40792307 | ||
| Ion transport mechanisms responsible for K+ secretion and the transepithelial voltage across marginal cells of stria vascularis in vitro | Q41679999 | ||
| Sidedness of action of loop diuretics and ouabain on nonsensory cells of utricle: a micro-Ussing chamber for inner ear tissues | Q42220210 | ||
| Effects of barium and ion substitutions in artificial blood on endocochlear potential | Q42435626 | ||
| Ultrastructural localization of the Na-K-Cl cotransporter in the lateral wall of the rabbit cochlear duct. | Q42437148 | ||
| Histochemical localization of carbonic anhydrase in the inner ear. | Q42456844 | ||
| The fast activating potassium current, I(K,f), in guinea-pig inner hair cells is regulated by protein kinase A. | Q42470969 | ||
| Gap junctions mediate glucose transport between GLUT1-positive and -negative cells in the spiral limbus of the rat cochlea | Q42493339 | ||
| Vesicular storage of adenosine triphosphate in the guinea-pig cochlear lateral wall and concentrations of ATP in the endolymph during sound exposure and hypoxia | Q42501676 | ||
| KCNJ10 (Kir4.1) potassium channel knockout abolishes endocochlear potential | Q42515610 | ||
| Maxi-K+ channel in plasma membrane of basal cells dissociated from the stria vascularis of gerbils | Q42522796 | ||
| The fine structure of spiral ligament cells relates to ion return to the stria and varies with place-frequency | Q42527121 | ||
| Functional beta2-adrenergic receptors are present in nonstrial tissues of the lateral wall in the gerbil cochlea | Q43688652 | ||
| P2X2 receptor mediates stimulation of parasensory cation absorption by cochlear outer sulcus cells and vestibular transitional cells. | Q43805341 | ||
| Compound heterozygous mutations in KvLQT1 cause Jervell and Lange-Nielsen syndrome | Q44019182 | ||
| Endolymphatic sodium homeostasis by Reissner's membrane | Q44451053 | ||
| Reduction of the endocochlear potential by the new "loop" diuretic, bumetanide | Q44702971 | ||
| Expression of an inwardly rectifying K+ channel, Kir5.1, in specific types of fibrocytes in the cochlear lateral wall suggests its functional importance in the establishment of endocochlear potential | Q44747842 | ||
| Mutations in GJA1 (connexin 43) are associated with non-syndromic autosomal recessive deafness | Q44884995 | ||
| Early effects of acetazolamide on anionic activities of the guinea pig endolymph: evidence for active function of carbonic anhydrase in the cochlea | Q45197049 | ||
| Accumulation of potassium in scala vestibuli perilymph of the mammalian cochlea | Q46179346 | ||
| Localization of pH regulating proteins H+ATPase and Cl-/HCO3- exchanger in the guinea pig inner ear. | Q46190394 | ||
| The Ca2+ activity of cochlear endolymph of the guinea pig and the effect of inhibitors | Q46211803 | ||
| The fine structure of freeze-fractured intercellular junctions in the guinea pig inner ear | Q46234495 | ||
| Vitamin D upregulates expression of ECaC1 mRNA in semicircular canal | Q46481249 | ||
| Ionic changes in cochlear endolymph of the guinea pig induced by acoustic injury | Q46589437 | ||
| Calcium transport mechanism in the endolymph of the chinchilla | Q46606484 | ||
| Respiratory rate and ATP content of stria vascularis of guinea pig in vitro | Q46669213 | ||
| Expression of the P2X(2) receptor subunit of the ATP-gated ion channel in the cochlea: implications for sound transduction and auditory neurotransmission. | Q46944206 | ||
| Inwardly rectifying K+ currents in intermediate cells in the cochlea of gerbils: a possible contribution to the endocochlear potential | Q47876563 | ||
| Connexin 26 gene linked to a dominant deafness | Q47991729 | ||
| Expression of the connexin43- and connexin45-encoding genes in the developing and mature mouse inner ear. | Q48032431 | ||
| Connexin26 mutations associated with the most common form of non-syndromic neurosensory autosomal recessive deafness (DFNB1) in Mediterraneans | Q48045551 | ||
| Round window pH manipulation alters the ototoxicity of systemic cisplatin | Q48105369 | ||
| Sensorineural hearing loss associated with hypoparathyroidism | Q48212222 | ||
| mRNA encoding 'ClC-K1, a kidney Cl(-)- channel' is expressed in marginal cells of the stria vascularis of rat cochlea: its possible contribution to Cl(-) currents | Q48892508 | ||
| Expression of connexin 30 in the developing mouse cochlea | Q48913468 | ||
| Neuro-otological findings in Pendred syndrome. | Q50484453 | ||
| Targeted disruption of mouse Pds provides insight about the inner-ear defects encountered in Pendred syndrome. | Q50493197 | ||
| Mice lacking the basolateral Na-K-2Cl cotransporter have impaired epithelial chloride secretion and are profoundly deaf. | Q50499859 | ||
| Mutation of the Na-K-Cl co-transporter gene Slc12a2 results in deafness in mice. | Q50500527 | ||
| Distribution of immunoreactive Na+,K+-ATPase in gerbil cochlea. | Q50559424 | ||
| Vitamin D deficiency--a new cause of cochlear deafness. | Q50592610 | ||
| Effects of noise on cochlear potentials and endolymph potassium concentration recorded with potassium-selective electrodes | Q50608923 | ||
| Potentials of outer hair cells and their membrane properties in cationic environments. | Q50943549 | ||
| K+ and Na+ absorption by outer sulcus epithelial cells. | Q51445689 | ||
| P433 | issue | Pt 1 | |
| P407 | language of work or name | English | Q1860 |
| P1104 | number of pages | 11 | |
| P304 | page(s) | 11-21 | |
| P577 | publication date | 2006-07-20 | |
| P1433 | published in | Journal of Physiology | Q7743612 |
| P1476 | title | Supporting sensory transduction: cochlear fluid homeostasis and the endocochlear potential | |
| P478 | volume | 576 |
| Q33495556 | A claudin-9-based ion permeability barrier is essential for hearing. |
| Q37402177 | A connected tale of claudins from the renal duct to the sensory system |
| Q30477247 | A major effect QTL on chromosome 18 for noise injury to the mouse cochlear lateral wall |
| Q90253619 | A microsensing system for the in vivo real-time detection of local drug kinetics |
| Q59132581 | A novel cancer syndrome caused by -deficiency in the golden Syrian hamster |
| Q30488731 | A systemic gentamicin pathway across the stria vascularis |
| Q30485384 | A zebrafish model for Waardenburg syndrome type IV reveals diverse roles for Sox10 in the otic vesicle |
| Q30484892 | ATP release through connexin hemichannels and gap junction transfer of second messengers propagate Ca2+ signals across the inner ear |
| Q30495800 | ATP-mediated cell-cell signaling in the organ of Corti: the role of connexin channels |
| Q47132491 | ATP1A3 mutations can cause progressive auditory neuropathy: a new gene of auditory synaptopathy |
| Q30482911 | Adenosine and the auditory system. |
| Q43477062 | Alterations in cochlear function during induced acute hyperinsulinemia in an animal model |
| Q28391552 | Altered inhibition of Cx26 hemichannels by pH and Zn2+ in the A40V mutation associated with keratitis-ichthyosis-deafness syndrome |
| Q90595610 | Aminoglycoside- and Cisplatin-Induced Ototoxicity: Mechanisms and Otoprotective Strategies |
| Q33899332 | Amplification mode differs along the length of the mouse cochlea as revealed by connexin 26 deletion from specific gap junctions |
| Q30449300 | Analgesic use and the risk of hearing loss in women |
| Q46641597 | Auditory Pathology in a Transgenic mtTFB1 Mouse Model of Mitochondrial Deafness |
| Q33632710 | Biochemical markers of bone turnover in benign paroxysmal positional vertigo |
| Q42452622 | Biodegradable polymeric coatings on cochlear implant surfaces and their influence on spiral ganglion cell survival |
| Q58610039 | Biomarkers of Systemic Inflammation and Risk of Incident Hearing Loss |
| Q30664961 | C-Raf deficiency leads to hearing loss and increased noise susceptibility |
| Q37893568 | Ca2+ homeostasis defects and hereditary hearing loss. |
| Q30483124 | Cadherins as targets for genetic diseases |
| Q50670746 | Canonical Wnt signaling regulates the proliferative expansion and differentiation of fibrocytes in the murine inner ear. |
| Q30370799 | Carotenoids, vitamin A, vitamin C, vitamin E, and folate and risk of self-reported hearing loss in women. |
| Q30452771 | Cell-type-specific roles of Na+/K+ ATPase subunits in Drosophila auditory mechanosensation |
| Q42127874 | Cellular characterization of Connexin26 and Connnexin30 expression in the cochlear lateral wall |
| Q49914916 | Co-deficiency of Lysosomal Mucolipins 3 and 1 in Cochlear Hair Cells Diminishes Outer Hair Cell Longevity and Accelerates Age-Related Hearing Loss. |
| Q42509693 | Co-localisation of K(ir)4.1 and AQP4 in rat and human cochleae reveals a gap in water channel expression at the transduction sites of endocochlear K(+) recycling routes |
| Q30460107 | Computational model of a circulation current that controls electrochemical properties in the mammalian cochlea |
| Q41527578 | Computer modeling defines the system driving a constant current crucial for homeostasis in the mammalian cochlea by integrating unique ion transports. |
| Q45871099 | Connexin 43 and hearing: possible implications for retrocochlear auditory processing |
| Q37652137 | Connexin expression patterns in diseased human corneas |
| Q36955841 | Connexin26 deafness associated mutations show altered permeability to large cationic molecules |
| Q30479250 | Connexin30 deficiency causes instrastrial fluid-blood barrier disruption within the cochlear stria vascularis |
| Q47989343 | Connexins and Disease |
| Q38266258 | Connexins and gap junctions in the inner ear--it's not just about K⁺ recycling |
| Q42116762 | Contractility in type III cochlear fibrocytes is dependent on non-muscle myosin II and intercellular gap junctional coupling |
| Q28302365 | Coordinated control of connexin 26 and connexin 30 at the regulatory and functional level in the inner ear |
| Q55188136 | Deafness and loss of cochlear hair cells in the absence of thyroid hormone transporters Slc16a2 (Mct8) and Slc16a10 (Mct10). |
| Q41968817 | Deafness induced by Connexin 26 (GJB2) deficiency is not determined by endocochlear potential (EP) reduction but is associated with cochlear developmental disorders |
| Q30471081 | Defining the cellular environment in the organ of Corti following extensive hair cell loss: a basis for future sensory cell replacement in the Cochlea |
| Q60912049 | Degeneration of saccular hair cells caused by MITF gene mutation |
| Q27303592 | Deletion of Tricellulin Causes Progressive Hearing Loss Associated with Degeneration of Cochlear Hair Cells |
| Q92177751 | Delivery of therapeutics to the inner ear: The challenge of the blood-labyrinth barrier |
| Q37580550 | Development of form and function in the mammalian cochlea. |
| Q43136229 | Developmentally regulated expression of ectonucleotidases NTPDase5 and NTPDase6 and UDP-responsive P2Y receptors in the rat cochlea |
| Q48119921 | Differences in molecular mechanisms of K+ clearance in the auditory sensory epithelium of birds and mammals. |
| Q30470991 | Different Cellular and Genetic Basis of Noise-Related Endocochlear Potential Reduction in CBA/J and BALB/cJ Mice |
| Q28115218 | Distinct roles of molecular chaperones HSP90α and HSP90β in the biogenesis of KCNQ4 channels |
| Q37101533 | Distribution of the Na,K-ATPase alpha subunit in the rat spiral ganglion and organ of corti. |
| Q50354000 | Does cochleostomy location influence electrode trajectory and intracochlear trauma? |
| Q45402338 | Drug-related nephrotoxic and ototoxic reactions : a link through a predictive mechanistic commonality. |
| Q50309186 | Duration of Analgesic Use and Risk of Hearing Loss in Women |
| Q26823188 | Early development of the vertebrate inner ear |
| Q48134020 | Effect of M-current modulation on mammalian vestibular responses to transient head motion. |
| Q37490444 | Effects of Long-Term Exercise on Age-Related Hearing Loss in Mice. |
| Q41845496 | Efficient siRNA transfection to the inner ear through the intact round window by a novel proteidic delivery technology in the chinchilla |
| Q40080564 | Emerging Gene Therapies for Genetic Hearing Loss |
| Q30484470 | Endocochlear potential depends on Cl- channels: mechanism underlying deafness in Bartter syndrome IV. |
| Q34761526 | Endolymphatic Na⁺ and K⁺ concentrations during cochlear growth and enlargement in mice lacking Slc26a4/pendrin |
| Q37217975 | Enhanced insulin sensitivity of gene-targeted mice lacking functional KCNQ1 |
| Q48673078 | Expression and distribution of creatine transporter and creatine kinase (brain isoform) in developing and mature rat cochlear tissues. |
| Q35725073 | Expression and localization of ryanodine receptors in the frog semicircular canal. |
| Q85637450 | Extracting energy from the inner ear |
| Q33754592 | Failure of Fluid Absorption in the Endolymphatic Sac Initiates Cochlear Enlargement that Leads to Deafness in Mice Lacking Pendrin Expression |
| Q28749118 | Finding new genes for non-syndromic hearing loss through an in silico prioritization study |
| Q34336019 | Fish and fatty acid consumption and the risk of hearing loss in women |
| Q92187667 | Forgotten Fibrocytes: A Neglected, Supporting Cell Type of the Cochlea With the Potential to be an Alternative Therapeutic Target in Hearing Loss |
| Q30413304 | Free radical stress-mediated loss of Kcnj10 protein expression in stria vascularis contributes to deafness in Pendred syndrome mouse model |
| Q26829380 | Functional analysis and regulation of purified connexin hemichannels |
| Q30466039 | Functional expression of P2X4 receptor in capillary endothelial cells of the cochlear spiral ligament and its role in regulating the capillary diameter |
| Q92002832 | GJB2 Mutations Linked to Hearing Loss Exhibit Differential Trafficking and Functional Defects as Revealed in Cochlear-Relevant Cells |
| Q21092155 | Gap junction mediated intercellular metabolite transfer in the cochlea is compromised in connexin30 null mice |
| Q30490087 | Gap-junction channels dysfunction in deafness and hearing loss |
| Q50317223 | Gap-junctional channel and hemichannel activity of two recently identified connexin 26 mutants associated with deafness. |
| Q30473829 | Gender differences in myogenic regulation along the vascular tree of the gerbil cochlea |
| Q35228799 | Genetics of recurrent vertigo and vestibular disorders |
| Q30464765 | Genome-wide linkage analyses identify Hfhl1 and Hfhl3 with frequency-specific effects on the hearing spectrum of NIH Swiss mice |
| Q37613089 | Genotype- and phenotype-guided management of congenital long QT syndrome |
| Q58696481 | Grxcr2 is required for stereocilia morphogenesis in the cochlea |
| Q42618413 | Hair Cell Transduction, Tuning, and Synaptic Transmission in the Mammalian Cochlea |
| Q35942220 | Head bobber: an insertional mutation causes inner ear defects, hyperactive circling, and deafness |
| Q47231195 | Hearing Loss in Adults. |
| Q90339565 | Hearing consequences in Gjb2 knock-in mice: implications for human p.V37I mutation |
| Q35243789 | Hearing loss associated with enlargement of the vestibular aqueduct: mechanistic insights from clinical phenotypes, genotypes, and mouse models |
| Q37655404 | How is the highly positive endocochlear potential formed? The specific architecture of the stria vascularis and the roles of the ion-transport apparatus |
| Q24655619 | Human adenylate kinase 2 deficiency causes a profound hematopoietic defect associated with sensorineural deafness |
| Q39273628 | Human diseases associated with connexin mutations. |
| Q30359618 | Hypertension, Diuretic Use, and Risk of Hearing Loss. |
| Q36816764 | Hypothyroidism of gene-targeted mice lacking Kcnq1. |
| Q30420205 | ILDR1 null mice, a model of human deafness DFNB42, show structural aberrations of tricellular tight junctions and degeneration of auditory hair cells |
| Q24646253 | Identification and characterization of pannexin expression in the mammalian cochlea |
| Q28506436 | Impaired stria vascularis integrity upon loss of E-cadherin in basal cells |
| Q37060221 | Impaired surface expression and conductance of the KCNQ4 channel lead to sensorineural hearing loss |
| Q38089731 | Inherited hearing loss: molecular genetics and diagnostic testing |
| Q48683488 | Inhibition of the heterotetrameric K+ channel KCNQ1/KCNE1 by the AMP-activated protein kinase |
| Q24318452 | Inner ear abnormalities in four patients with dRTA and SNHL: clinical and genetic heterogeneity |
| Q30439408 | Inner ear supporting cells: rethinking the silent majority. |
| Q41988399 | Inner ear tissue remodeling and ion homeostasis gene alteration in murine chronic otitis media |
| Q48097842 | Intrafamilial variable hearing loss in TRPV4 induced spinal muscular atrophy |
| Q30380467 | Intratympanic Steroid Treatments May Improve Hearing via Ion Homeostasis Alterations and Not Immune Suppression |
| Q57178143 | Investigating Potassium Channels in Budding Yeast: A Genetic Sandbox |
| Q30396787 | KCNK5 channels mostly expressed in cochlear outer sulcus cells are indispensable for hearing |
| Q58797137 | Label-free quantitative mass spectrometry analysis of differential protein expression in the developing cochlear sensory epithelium |
| Q28397863 | Lead roles for supporting actors: critical functions of inner ear supporting cells |
| Q28391018 | Live imaging the phagocytic activity of inner ear supporting cells in response to hair cell death |
| Q42794956 | Localization of gentamicin uptake in the acutely isolated inner ear of the rat. |
| Q28593346 | Loss of Sox9 in the periotic mesenchyme affects mesenchymal expansion and differentiation, and epithelial morphogenesis during cochlea development in the mouse |
| Q30494661 | Loss of cochlear HCO3- secretion causes deafness via endolymphatic acidification and inhibition of Ca2+ reabsorption in a Pendred syndrome mouse model |
| Q46474342 | Mammalian prestin is a weak Cl⁻/HCO₃⁻ electrogenic antiporter |
| Q99248422 | Mechanically facilitated micro-fluid mixing in the organ of Corti |
| Q30480940 | Mechanisms and genes in human strial presbycusis from animal models |
| Q36792635 | Mechanotransduction and auditory transduction in Drosophila. |
| Q43258209 | Melanin precursors prevent premature age-related and noise-induced hearing loss in albino mice |
| Q27001531 | Modeling auditory coding: from sound to spikes |
| Q37886840 | Modulation of connexin signaling by bacterial pathogens and their toxins |
| Q35659340 | Molecular architecture of the stria vascularis membrane transport system, which is essential for physiological functions of the mammalian cochlea. |
| Q37294043 | Molecular bases of K(+) secretory cells in the inner ear: shared and distinct features between birds and mammals |
| Q38353200 | Molecular basis of hair cell loss |
| Q30467847 | Molecular biology of hearing |
| Q37383087 | Mouse models for human hereditary deafness |
| Q35557773 | Mouse models for pendrin-associated loss of cochlear and vestibular function |
| Q41839940 | Murine middle ear inflammation and ion homeostasis gene expression |
| Q48198890 | Mutations in L-type amino acid transporter-2 support SLC7A8 as a novel gene involved in Age-Related Hearing Loss |
| Q50354500 | NKCCs in the fibrocytes of the spiral ligament are silent on the unidirectional K⁺ transport that controls the electrochemical properties in the mammalian cochlea |
| Q30459309 | NOS inhibition enhances myogenic tone by increasing rho-kinase mediated Ca2+ sensitivity in the male but not the female gerbil spiral modiolar artery |
| Q41526695 | Non-autonomous Cellular Responses to Ototoxic Drug-Induced Stress and Death |
| Q30365442 | Organ of Corti and Stria Vascularis: Is there an Interdependence for Survival? |
| Q55618045 | PECONPI: a novel software for uncovering pathogenic copy number variations in non-syndromic sensorineural hearing loss and other genetically heterogeneous disorders. |
| Q42153064 | Perinatal Gjb2 gene transfer rescues hearing in a mouse model of hereditary deafness |
| Q92616899 | Petrosal morphology and cochlear function in Mesozoic stem therians |
| Q36680215 | Phenotypic variability of CLDN14 mutations causing DFNB29 hearing loss in the Pakistani population |
| Q57047656 | Pilot Study of Audiometric Patterns in Fuchs Corneal Dystrophy |
| Q30413390 | Potassium ion movement in the inner ear: insights from genetic disease and mouse models |
| Q37142101 | Precise toxigenic ablation of intermediate cells abolishes the "battery" of the cochlear duct |
| Q36931773 | Prevalence and potential genetic determinants of sensorineural deafness in KCNQ1 homozygosity and compound heterozygosity |
| Q46338409 | Preventative effect of various fluids used in the epitympanic bulla on deterioration of cochlear function during labyrinthectomy |
| Q30530777 | Probing the Xenopus laevis inner ear transcriptome for biological function |
| Q28506642 | Progressive Hearing Loss in Mice Carrying a Mutation in Usp53. |
| Q40609376 | Prospective Study of Gastroesophageal Reflux, Use of Proton Pump Inhibitors and H2-Receptor Antagonists, and Risk of Hearing Loss |
| Q46160334 | Protection of the cochlea by ascorbic acid in noise trauma |
| Q92879640 | Purinergic Signaling and Cochlear Injury-Targeting the Immune System? |
| Q30491908 | Purinergic signaling in the inner ear. |
| Q30355174 | QTL Mapping of Endocochlear Potential Differences between C57BL/6J and BALB/cJ mice. |
| Q30419420 | Quantitative analysis linking inner hair cell voltage changes and postsynaptic conductance change: a modelling study |
| Q30458329 | Rabconnectin3α promotes stable activity of the H+ pump on synaptic vesicles in hair cells |
| Q26851254 | Reactive oxygen species, apoptosis, and mitochondrial dysfunction in hearing loss |
| Q30485597 | Recent findings and emerging questions in cochlear noise injury |
| Q37881216 | Regulation of sodium transport in the inner ear. |
| Q30465212 | Relative time course of degeneration of different cochlear structures in the CD/1 mouse model of accelerated aging |
| Q30474377 | Role of adenosine kinase in cochlear development and response to noise |
| Q30479860 | Role of nitric oxide on purinergic signalling in the cochlea |
| Q36180664 | Ryanodine-induced vasoconstriction of the gerbil spiral modiolar artery depends on the Ca2+ sensitivity but not on Ca2+ sparks or BK channels |
| Q30481589 | Selective activation of nuclear factor kappa B in the cochlea by sensory and inflammatory stress |
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