scholarly article | Q13442814 |
P356 | DOI | 10.1073/PNAS.1606387114 |
P8608 | Fatcat ID | release_atxrcib4p5hxnmlopjb4n5sz7u |
P932 | PMC publication ID | 5240680 |
P698 | PubMed publication ID | 28028229 |
P50 | author | Ajoy Vincent | Q42844960 |
Susanne Kohl | Q47502299 | ||
Wei-Chieh Chiang | Q81702226 | ||
Anna Skorczyk-Werner | Q90432646 | ||
Maciej Krawczyński | Q19690556 | ||
P2093 | author name string | Elise Héon | |
Jonathan H Lin | |||
Randal J Kaufman | |||
Bernd Wissinger | |||
Stephen H Tsang | |||
Priscilla Chan | |||
P2860 | cites work | ATF6alpha induces XBP1-independent expansion of the endoplasmic reticulum | Q37186859 |
Targeted overexpression of parathyroid hormone-related peptide in chondrocytes causes chondrodysplasia and delayed endochondral bone formation | Q37332979 | ||
Protein misfolding in the endoplasmic reticulum as a conduit to human disease | Q38704807 | ||
Role of endoplasmic reticulum stress in light-induced photoreceptor degeneration in mice | Q39231671 | ||
ATF6alpha optimizes long-term endoplasmic reticulum function to protect cells from chronic stress | Q42518206 | ||
Robust Endoplasmic Reticulum-Associated Degradation of Rhodopsin Precedes Retinal Degeneration. | Q43214685 | ||
Activation of ATF6 and an ATF6 DNA binding site by the endoplasmic reticulum stress response. | Q45345766 | ||
Endoplasmic reticulum stress is activated in light-induced retinal degeneration | Q46955913 | ||
Transcriptional induction of mammalian ER quality control proteins is mediated by single or combined action of ATF6alpha and XBP1 | Q80979487 | ||
Mammalian transcription factor ATF6 is synthesized as a transmembrane protein and activated by proteolysis in response to endoplasmic reticulum stress | Q22010800 | ||
ER stress induces cleavage of membrane-bound ATF6 by the same proteases that process SREBPs | Q24290776 | ||
XBP1 mRNA is induced by ATF6 and spliced by IRE1 in response to ER stress to produce a highly active transcription factor | Q24292102 | ||
The unfolded protein response in retinal vascular diseases: implications and therapeutic potential beyond protein folding | Q26852080 | ||
Mutations in the unfolded protein response regulator ATF6 cause the cone dysfunction disorder achromatopsia | Q28115716 | ||
Perk is essential for translational regulation and cell survival during the unfolded protein response | Q28140062 | ||
Translational control is required for the unfolded protein response and in vivo glucose homeostasis | Q28204066 | ||
IRE1 couples endoplasmic reticulum load to secretory capacity by processing the XBP-1 mRNA | Q28214814 | ||
Regulated translation initiation controls stress-induced gene expression in mammalian cells | Q28506388 | ||
ER stress regulation of ATF6 localization by dissociation of BiP/GRP78 binding and unmasking of Golgi localization signals | Q28646129 | ||
The unfolded protein response: from stress pathway to homeostatic regulation | Q29547396 | ||
IRE1 signaling affects cell fate during the unfolded protein response | Q29615502 | ||
Adaptation to ER stress is mediated by differential stabilities of pro-survival and pro-apoptotic mRNAs and proteins | Q33262919 | ||
Comparison of nonsense-mediated mRNA decay efficiency in various murine tissues | Q33390501 | ||
Endoplasmic reticulum stress and the unfolded protein responses in retinal degeneration | Q34005691 | ||
A prospective longitudinal study of retinal structure and function in achromatopsia. | Q34166706 | ||
Activation of mammalian unfolded protein response is compatible with the quality control system operating in the endoplasmic reticulum | Q34358672 | ||
Photoreceptor structure and function in patients with congenital achromatopsia. | Q35247580 | ||
ATF6 Is Mutated in Early Onset Photoreceptor Degeneration With Macular Involvement | Q35745744 | ||
The IRE1α/XBP1s Pathway Is Essential for the Glucose Response and Protection of β Cells. | Q35808715 | ||
Mutation of ATF6 causes autosomal recessive achromatopsia | Q35929399 | ||
In Vivo Visualization of Endoplasmic Reticulum Stress in the Retina Using the ERAI Reporter Mouse | Q36232562 | ||
Selective activation of ATF6 and PERK endoplasmic reticulum stress signaling pathways prevent mutant rhodopsin accumulation | Q36327872 | ||
Induction of endoplasmic reticulum stress genes, BiP and chop, in genetic and environmental models of retinal degeneration | Q36391530 | ||
Stress-independent activation of XBP1s and/or ATF6 reveals three functionally diverse ER proteostasis environments | Q37124391 | ||
P433 | issue | 2 | |
P407 | language of work or name | English | Q1860 |
P921 | main subject | achromatopsia | Q432396 |
P304 | page(s) | 400-405 | |
P577 | publication date | 2016-12-27 | |
P1433 | published in | Proceedings of the National Academy of Sciences of the United States of America | Q1146531 |
P1476 | title | Achromatopsia mutations target sequential steps of ATF6 activation | |
P478 | volume | 114 |
Q47750345 | Achromatopsia: clinical features, molecular genetics, animal models and therapeutic options |
Q89999387 | Atf6α impacts cell number by influencing survival, death and proliferation |
Q45933371 | Autosomal recessive cone-rod dystrophy can be caused by mutations in the ATF6 gene. |
Q38653861 | ER stress and the unfolded protein response in neurodegeneration |
Q88869497 | ER stress and unfolded protein response in ocular health and disease |
Q92333949 | ERp18 regulates activation of ATF6α during unfolded protein response |
Q47404960 | Emerging therapeutic targets currently under investigation for the treatment of systemic amyloidosis |
Q92093362 | Establishment and validation of an endoplasmic reticulum stress reporter to monitor zebrafish ATF6 activity in development and disease |
Q39016569 | Gene therapy for achromatopsia. |
Q52609398 | Loss of XBP1 accelerates age-related decline in retinal function and neurodegeneration. |
Q92301861 | Pathomechanisms of ATF6-Associated Cone Photoreceptor Diseases |
Q56530196 | Pharmacologic ATF6 activating compounds are metabolically activated to selectively modify endoplasmic reticulum proteins |
Q41583320 | Physiological/pathological ramifications of transcription factors in the unfolded protein response |
Q33653691 | Recent Insights into the Role of Unfolded Protein Response in ER Stress in Health and Disease |
Q39396098 | Regulating Secretory Proteostasis through the Unfolded Protein Response: From Function to Therapy |
Q91633568 | The unfolded protein response in metazoan development |
Q50026168 | The unfolded protein response regulator ATF6 promotes mesodermal differentiation. |
Q55498838 | Unfolding the Endoplasmic Reticulum of a Social Amoeba: Dictyostelium discoideum as a New Model for the Study of Endoplasmic Reticulum Stress. |
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