scholarly article | Q13442814 |
P2093 | author name string | Michael E Cheetham | |
David A Parfitt | |||
Dalila Bevilacqua | |||
Dimitra Athanasiou | |||
Monica Aguilà | |||
Sergey S Novoselov | |||
P2860 | cites work | Mechanisms of cell death in rhodopsin retinitis pigmentosa: implications for therapy | Q21710681 |
A membrane protein complex mediates retro-translocation from the ER lumen into the cytosol | Q24297732 | ||
Structure and intermolecular interactions of the luminal dimerization domain of human IRE1alpha | Q24297815 | ||
A dual role for EDEM1 in the processing of rod opsin | Q24320047 | ||
The chaperone-mediated autophagy receptor organizes in dynamic protein complexes at the lysosomal membrane | Q24646454 | ||
Tauroursodeoxycholic acid preservation of photoreceptor structure and function in the rd10 mouse through postnatal day 30 | Q24649167 | ||
Bile acids in treatment of ocular disease | Q24653326 | ||
One step at a time: endoplasmic reticulum-associated degradation | Q24658302 | ||
The axonal transport of mitochondria | Q27007553 | ||
Inactivation of VCP/ter94 suppresses retinal pathology caused by misfolded rhodopsin in Drosophila | Q27346679 | ||
AAA-ATPase p97/Cdc48p, a cytosolic chaperone required for endoplasmic reticulum-associated protein degradation | Q27939982 | ||
The Chaperone Environment at the Cytoplasmic Face of the Endoplasmic Reticulum Can Modulate Rhodopsin Processing and Inclusion Formation | Q28117679 | ||
Adapting proteostasis for disease intervention | Q28131818 | ||
Nuclear gene OPA1, encoding a mitochondrial dynamin-related protein, is mutated in dominant optic atrophy | Q28140286 | ||
Molecular chaperones in the cytosol: from nascent chain to folded protein | Q28205903 | ||
Adult-onset primary open-angle glaucoma caused by mutations in optineurin | Q28217964 | ||
Mitochondrial dysfunction as a cause of optic neuropathies | Q28242704 | ||
Mitochondrial DNA mutation associated with Leber's hereditary optic neuropathy | Q28292821 | ||
Processing of optineurin in neuronal cells | Q28570083 | ||
XBP-1 Regulates a Subset of Endoplasmic Reticulum Resident Chaperone Genes in the Unfolded Protein Response | Q28585314 | ||
ER stress regulation of ATF6 localization by dissociation of BiP/GRP78 binding and unmasking of Golgi localization signals | Q28646129 | ||
The Hsp70 and Hsp60 chaperone machines | Q29547601 | ||
IRE1 signaling affects cell fate during the unfolded protein response | Q29615502 | ||
Retinitis pigmentosa | Q29616538 | ||
Rhodopsin: the functional significance of asn-linked glycosylation and other post-translational modifications | Q30382885 | ||
Clearance of Rhodopsin(P23H) aggregates requires the ERAD effector VCP. | Q43185410 | ||
Calnexin is not essential for mammalian rod opsin biogenesis | Q43218251 | ||
Retinal glial (Müller ) cells: sensing and responding to tissue stretch | Q43247672 | ||
Regulated heat shock protein 27 expression in human retinal pigment epithelium | Q43693084 | ||
Injury to retinal ganglion cells induces expression of the small heat shock protein Hsp27 in the rat visual system | Q43948430 | ||
Blue light dose distribution and retinitis pigmentosa visual field defects: an hypothesis | Q44413738 | ||
Expression of heat shock transcription factors and heat shock protein 72 in rat retina after intravitreal injection of low dose N-methyl-D-aspartate. | Q44568146 | ||
Clinical trial of docosahexaenoic acid in patients with retinitis pigmentosa receiving vitamin A treatment | Q45056943 | ||
Correction of the disease phenotype of myocilin-causing glaucoma by a natural osmolyte | Q46113790 | ||
Leukemia inhibitory factor extends the lifespan of injured photoreceptors in vivo. | Q46192796 | ||
Prevention of age-related macular degeneration-like retinopathy by rapamycin in rats. | Q46476515 | ||
Ligand-independent dimerization activates the stress response kinases IRE1 and PERK in the lumen of the endoplasmic reticulum | Q50336389 | ||
Hsp27 phosphorylation in experimental glaucoma. | Q51740428 | ||
Immunostaining of heat shock proteins in the retina and optic nerve head of normal and glaucomatous eyes. | Q53913933 | ||
Protein Disulfide Isomerase Acts as a Redox-Dependent Chaperone to Unfold Cholera Toxin | Q57180002 | ||
Primary open-angle glaucoma | Q57728691 | ||
Hyperthermia protects against light damage in the rat retina | Q67942688 | ||
Morphologic changes in the lamina cribrosa correlated with neural loss in open-angle glaucoma | Q71722798 | ||
Endothelin receptor expression in the normal and injured spinal cord: potential involvement in injury-induced ischemia and gliosis | Q73198787 | ||
Retinal ganglion cell protection with geranylgeranylacetone, a heat shock protein inducer, in a rat glaucoma model | Q73316526 | ||
Attenuation of diabetic retinopathy by the molecular chaperone-inducer amino acid analogue canavanine in streptozotocin-diabetic rats | Q77565005 | ||
Degenerative and apoptotic events at retinal and optic nerve level after experimental induction of ocular hypertension | Q79624489 | ||
Antioxidants slow photoreceptor cell death in mouse models of retinitis pigmentosa | Q80372689 | ||
Genetic heterogeneity in Usher syndrome | Q80565750 | ||
Transcriptional induction of mammalian ER quality control proteins is mediated by single or combined action of ATF6alpha and XBP1 | Q80979487 | ||
Cellular osmolytes reduce lens epithelial cell death and alleviate cataract formation in galactosemic rats | Q80984872 | ||
Crystallin distribution in Bruch's membrane-choroid complex from AMD and age-matched donor eyes | Q81818734 | ||
Lack of scientific rationale for use of valproic acid for retinitis pigmentosa | Q82737104 | ||
HSP70, the earliest-induced gene in the zebrafish retina during optic nerve regeneration: its role in cell survival | Q83455211 | ||
Valproic acid treatment may be harmful in non-dominant forms of retinitis pigmentosa | Q84120502 | ||
Calnexin deficiency leads to dysmyelination | Q30431936 | ||
Autophagy and exosomes in the aged retinal pigment epithelium: possible relevance to drusen formation and age-related macular degeneration | Q30856906 | ||
Induction of heat shock protein 72 protects retinal ganglion cells in a rat glaucoma model | Q30990834 | ||
Retinal preconditioning and the induction of heat-shock protein 27. | Q31132630 | ||
Systemic rapamycin inhibits retinal and choroidal neovascularization in mice | Q31137912 | ||
Retinal pigment epithelium is protected against apoptosis by alphaB-crystallin. | Q33185028 | ||
Retinal ganglion cell protection with geranylgeranylacetone, a heat shock protein inducer, in a rat glaucoma model | Q33198398 | ||
The cyclophilin homolog ninaA is a tissue-specific integral membrane protein required for the proper synthesis of a subset of Drosophila rhodopsins | Q33262317 | ||
Angiogenic and antiangiogenic factors in proliferative diabetic retinopathy. | Q33316526 | ||
The feedback pathway from horizontal cells to cones. A mini review with a look ahead | Q33682066 | ||
Light-induced phosphorylation of crystallins in the retinal pigment epithelium | Q33752644 | ||
Restoration of visual function in P23H rhodopsin transgenic rats by gene delivery of BiP/Grp78 | Q33778232 | ||
Constituents of bile, bilirubin and TUDCA, protect against oxidative stress-induced retinal degeneration | Q33853136 | ||
The role of oxidative stress in the pathogenesis of age-related macular degeneration. | Q34060719 | ||
The fundamental plan of the retina | Q34088683 | ||
The cellular fate of mutant rhodopsin: quality control, degradation and aggresome formation. | Q34135152 | ||
Protein folding in the cytoplasm and the heat shock response | Q34152827 | ||
Tauroursodeoxycholic acid prevents retinal degeneration in transgenic P23H rats. | Q34179718 | ||
ER stress in retinal degeneration in S334ter Rho rats | Q34202842 | ||
Glycopeptide specificity of the secretory protein folding sensor UDP-glucose glycoprotein:glucosyltransferase. | Q34236548 | ||
Mutations within the rhodopsin gene in patients with autosomal dominant retinitis pigmentosa | Q34239582 | ||
Vascular endothelial growth factor in ocular fluid of patients with diabetic retinopathy and other retinal disorders | Q34292807 | ||
The neuronal organization of the retina | Q34307217 | ||
Regulation of retinal proteome by topical antiglaucomatous eye drops in an inherited glaucoma rat model | Q34335584 | ||
Pharmacological chaperone-mediated in vivo folding and stabilization of the P23H-opsin mutant associated with autosomal dominant retinitis pigmentosa | Q34338708 | ||
Identification of a novel adult-onset primary open-angle glaucoma (POAG) gene on 5q22.1. | Q34389060 | ||
Identification of a gene that causes primary open angle glaucoma. | Q34414141 | ||
Defective intracellular transport is the molecular basis of rhodopsin-dependent dominant retinal degeneration | Q34535642 | ||
Protein translocation across the eukaryotic endoplasmic reticulum and bacterial plasma membranes | Q34719604 | ||
Molecular clustering identifies complement and endothelin induction as early events in a mouse model of glaucoma | Q34755301 | ||
Myocilin and glaucoma: facts and ideas. | Q34768697 | ||
Reduction of ER stress via a chemical chaperone prevents disease phenotypes in a mouse model of primary open angle glaucoma. | Q35187142 | ||
Mitochondrial proteomics of the retinal pigment epithelium at progressive stages of age-related macular degeneration | Q35423355 | ||
Effect of rapamycin on the fate of P23H opsin associated with retinitis pigmentosa (an American Ophthalmological Society thesis). | Q35662681 | ||
Sodium 4-phenylbutyrate acts as a chemical chaperone on misfolded myocilin to rescue cells from endoplasmic reticulum stress and apoptosis | Q42615777 | ||
Characterization of an ERAD pathway for nonglycosylated BiP substrates, which require Herp | Q42820056 | ||
Therapeutic potential of valproic acid for retinitis pigmentosa | Q84582883 | ||
IRE1 directs proteasomal and lysosomal degradation of misfolded rhodopsin | Q35790874 | ||
Crosstalk between Hsp70 molecular chaperone, lysosomes and proteasomes in autophagy-mediated proteolysis in human retinal pigment epithelial cells | Q35893349 | ||
Modulation of neurodegeneration by molecular chaperones | Q35990274 | ||
ER stress is involved in T17M rhodopsin-induced retinal degeneration. | Q36077630 | ||
The retinal pigment epithelium in visual function | Q36178984 | ||
Selective activation of ATF6 and PERK endoplasmic reticulum stress signaling pathways prevent mutant rhodopsin accumulation | Q36327872 | ||
Induction of endoplasmic reticulum stress genes, BiP and chop, in genetic and environmental models of retinal degeneration | Q36391530 | ||
Glucose-regulated protein 94 triage of mutant myocilin through endoplasmic reticulum-associated degradation subverts a more efficient autophagic clearance mechanism | Q36418920 | ||
Light and inherited retinal degeneration | Q36481342 | ||
Diseases caused by defects in the visual cycle: retinoids as potential therapeutic agents | Q36591612 | ||
Mutations in the X-linked retinitis pigmentosa genes RPGR and RP2 found in 8.5% of families with a provisional diagnosis of autosomal dominant retinitis pigmentosa | Q36683600 | ||
Perspective on genes and mutations causing retinitis pigmentosa | Q36734545 | ||
Mechanisms of disease II: cellular protein quality control. | Q36748835 | ||
Antiapoptotic properties of α-crystallin-derived peptide chaperones and characterization of their uptake transporters in human RPE cells | Q36784092 | ||
Blood-retinal barrier in hypoxic ischaemic conditions: basic concepts, clinical features and management | Q37304800 | ||
Novel lipofuscin bisretinoids prominent in human retina and in a model of recessive Stargardt disease | Q37339031 | ||
Suppression of retinal degeneration in Drosophila by stimulation of ER-associated degradation | Q37359601 | ||
Involvement of Müller glial cells in epiretinal membrane formation | Q37470227 | ||
Mammalian macroautophagy at a glance | Q37491912 | ||
Alpha B-crystallin is a small heat shock protein | Q37494057 | ||
Retinal light damage: mechanisms and protection | Q37642126 | ||
Photoreceptor degeneration: genetic and mechanistic dissection of a complex trait | Q37704937 | ||
Mitochondrial dysfunction in glaucoma and emerging bioenergetic therapies. | Q37778419 | ||
Autophagy in the retina: a potential role in age-related macular degeneration | Q37969947 | ||
The genomic response to retinal disease and injury: evidence for endothelin signaling from photoreceptors to glia. | Q38326728 | ||
Accumulation of mutant myocilins in ER leads to ER stress and potential cytotoxicity in human trabecular meshwork cells | Q38518594 | ||
Rod vision is controlled by dopamine-dependent sensitization of rod bipolar cells by GABA. | Q38757734 | ||
BiP prevents rod opsin aggregation | Q39303756 | ||
XPORT-dependent transport of TRP and rhodopsin. | Q39440497 | ||
Molecular mechanisms of rhodopsin retinitis pigmentosa and the efficacy of pharmacological rescue | Q39774938 | ||
Calnexin improves the folding efficiency of mutant rhodopsin in the presence of pharmacological chaperone 11-cis-retinal | Q39791822 | ||
Pharmacological manipulation of gain-of-function and dominant-negative mechanisms in rhodopsin retinitis pigmentosa. | Q39960161 | ||
Oxidative stress affects the junctional integrity of retinal pigment epithelial cells. | Q40595305 | ||
Rapid degradation of a large fraction of newly synthesized proteins by proteasomes. | Q40883590 | ||
Calnexin is essential for rhodopsin maturation, Ca2+ regulation, and photoreceptor cell survival | Q42266704 | ||
Prevention of autosomal dominant retinitis pigmentosa by systemic drug therapy targeting heat shock protein 90 (Hsp90) | Q42408195 | ||
Hsp25 and -90 immunoreactivity in the normal rat eye. | Q42512250 | ||
P433 | issue | 13 | |
P407 | language of work or name | English | Q1860 |
P304 | page(s) | 2008-2017 | |
P577 | publication date | 2013-05-15 | |
P1433 | published in | FEBS Letters | Q1388051 |
P1476 | title | The cell stress machinery and retinal degeneration | |
P478 | volume | 587 |
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