Transneuronal propagation of mutant huntingtin contributes to non-cell autonomous pathology in neurons

scientific article

Transneuronal propagation of mutant huntingtin contributes to non-cell autonomous pathology in neurons is …
instance of (P31):
scholarly articleQ13442814

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P356DOI10.1038/NN.3761
P698PubMed publication ID25017010
P5875ResearchGate publication ID263897142

P50authorPaolo BottaQ79611880
María Soledad EspositoQ39698421
P2093author name stringMatthias Müller
Tewis Bouwmeester
Sascha Fuchs
Andreas Lüthi
Silvia Arber
Claus Rieker
Francesco Paolo Di Giorgio
Dorothee Bleckmann
Herman van der Putten
Ivan Galimberti
Mario Bernhard
Eline Pecho-Vrieseling
Chris Goldstein
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Pathological cell-cell interactions elicited by a neuropathogenic form of mutant Huntingtin contribute to cortical pathogenesis in HD mice.Q45296827
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TR-FRET-based duplex immunoassay reveals an inverse correlation of soluble and aggregated mutant huntingtin in huntington's diseaseQ45306486
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Pathological α-synuclein transmission initiates Parkinson-like neurodegeneration in nontransgenic miceQ29620597
Extensive early motor and non-motor behavioral deficits are followed by striatal neuronal loss in knock-in Huntington's disease miceQ30437914
Human embryonic stem cell-derived GABA neurons correct locomotion deficits in quinolinic acid-lesioned mice.Q30512860
Proteolysis of mutant huntingtin produces an exon 1 fragment that accumulates as an aggregated protein in neuronal nuclei in Huntington diseaseQ33726473
Huntington disease models and human neuropathology: similarities and differencesQ33760994
Huntington's disease: from molecular pathogenesis to clinical treatmentQ33773061
Evaluation of the therapeutic usefulness of botulinum neurotoxin B, C1, E, and F compared with the long lasting type A. Basis for distinct durations of inhibition of exocytosis in central neuronsQ34154552
Dysfunctional behavioral modulation of corticostriatal communication in the R6/2 mouse model of Huntington's diseaseQ34442696
Atg4b-dependent autophagic flux alleviates Huntington's disease progressionQ34827331
Prions hijack tunnelling nanotubes for intercellular spreadQ34938949
Exogenous α-synuclein fibrils induce Lewy body pathology leading to synaptic dysfunction and neuron deathQ35484581
Identification of the major steps in botulinum toxin actionQ35639122
DARPP-32: an integrator of neurotransmissionQ35639141
Predicting regional neurodegeneration from the healthy brain functional connectomeQ35991719
Botulinum neurotoxin A blocks synaptic vesicle exocytosis but not endocytosis at the nerve terminalQ36313397
Aberrant splicing of HTT generates the pathogenic exon 1 protein in Huntington diseaseQ36598263
Huntington's disease: progress and potential in the fieldQ37016096
Full-length human mutant huntingtin with a stable polyglutamine repeat can elicit progressive and selective neuropathogenesis in BACHD miceQ37072467
Neural transplants in patients with Huntington's disease undergo disease-like neuronal degenerationQ37268805
Protein aggregates in Huntington's disease.Q37540988
Neuronal activity regulates extracellular tau in vivoQ37630201
The transcellular spread of cytosolic amyloids, prions, and prionoidsQ37671889
Pathophysiology of Huntington's disease: time-dependent alterations in synaptic and receptor function.Q37930190
Huntington's disease and the striatal medium spiny neuron: cell-autonomous and non-cell-autonomous mechanisms of diseaseQ37996350
Molecular logic of neocortical projection neuron specification, development and diversityQ38150734
Cell-to-cell transmission of pathogenic proteins in neurodegenerative diseasesQ38185934
Physiological release of endogenous tau is stimulated by neuronal activity.Q39560268
P2507corrigendum / erratumAuthor Correction: Transneuronal propagation of mutant huntingtin contributes to non-cell autonomous pathology in neuronsQ90295292
P433issue8
P407language of work or nameEnglishQ1860
P304page(s)1064-1072
P577publication date2014-07-13
P1433published inNature NeuroscienceQ1535359
P1476titleTransneuronal propagation of mutant huntingtin contributes to non-cell autonomous pathology in neurons
P478volume17

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