| scholarly article | Q13442814 |
| P50 | author | Steve Vucic | Q66904917 |
| Matthew C Kiernan | Q75660683 | ||
| P2093 | author name string | Susanna B Park | |
| P2860 | cites work | A quantitative description of membrane current and its application to conduction and excitation in nerve | Q22337072 |
| From ionic currents to molecular mechanisms: the structure and function of voltage-gated sodium channels | Q28143653 | ||
| International Union of Pharmacology. XLVII. Nomenclature and structure-function relationships of voltage-gated sodium channels | Q28289125 | ||
| Identification and characterization of a spinal muscular atrophy-determining gene | Q29547495 | ||
| Gene expression profile of spinal motor neurons in sporadic amyotrophic lateral sclerosis | Q31143351 | ||
| Electrophysiological study on limb myokymia in three women | Q33628765 | ||
| Phenotypic variants of autoimmune peripheral nerve hyperexcitability | Q33960383 | ||
| Androgen receptor gene mutations in X-linked spinal and bulbar muscular atrophy | Q34023072 | ||
| Progressive proximal spinal and bulbar muscular atrophy of late onset. A sex-linked recessive trait | Q34051849 | ||
| Morvan's syndrome: peripheral and central nervous system and cardiac involvement with antibodies to voltage-gated potassium channels | Q34101039 | ||
| Resurgence of sodium channel research | Q34142210 | ||
| Voltage-gated sodium channels at 60: structure, function and pathophysiology | Q34265707 | ||
| Excitability of human axons | Q34341990 | ||
| Immunological associations of acquired neuromyotonia (Isaacs' syndrome). Report of five cases and literature review | Q34362450 | ||
| Acute tetrodotoxin-induced neurotoxicity after ingestion of puffer fish | Q34397874 | ||
| Autoantibodies detected to expressed K+ channels are implicated in neuromyotonia | Q34416092 | ||
| Muscle cramps | Q34419913 | ||
| Anoxic and Ischemic Injury of Myelinated Axons in CNS White Matter: From Mechanistic Concepts to Therapeutics | Q34452140 | ||
| Depolarization changes the mechanism of accommodation in rat and human motor axons | Q34483589 | ||
| Early Functional Impairment of Sensory-Motor Connectivity in a Mouse Model of Spinal Muscular Atrophy | Q34602175 | ||
| Dissociated small hand muscle atrophy in amyotrophic lateral sclerosis: frequency, extent, and specificity | Q34743713 | ||
| Human iPSC-derived motoneurons harbouring TARDBP or C9ORF72 ALS mutations are dysfunctional despite maintaining viability | Q35114316 | ||
| Excitability properties of motor axons in patients with spontaneous motor unit activity | Q35572376 | ||
| Axonal excitability properties in amyotrophic lateral sclerosis | Q47202111 | ||
| Latent addition in motor and sensory fibres of human peripheral nerve | Q47914397 | ||
| Differences in behaviour of sensory and motor axons following release of ischaemia | Q48142798 | ||
| Presynaptic rat Kv1.2 channels suppress synaptic terminal hyperexcitability following action potential invasion | Q48294517 | ||
| Strength-duration properties of sensory and motor axons in amyotrophic lateral sclerosis | Q48454083 | ||
| Axonal ion channel dysfunction in c9orf72 familial amyotrophic lateral sclerosis | Q48460652 | ||
| Novel threshold tracking techniques suggest that cortical hyperexcitability is an early feature of motor neuron disease | Q48474459 | ||
| Evidence for axonal membrane hyperpolarization in multifocal motor neuropathy with conduction block | Q48672941 | ||
| Membrane properties in chronic inflammatory demyelinating polyneuropathy | Q48716624 | ||
| Axonal dysfunction with voltage gated potassium channel complex antibodies | Q48717846 | ||
| Increased variability of axonal excitability in amyotrophic lateral sclerosis | Q48721841 | ||
| Riluzole exerts central and peripheral modulating effects in amyotrophic lateral sclerosis. | Q48726185 | ||
| Peripheral motor axons of SOD1(G127X) mutant mice are susceptible to activity-dependent degeneration. | Q48731211 | ||
| Upregulation of persistent sodium conductances in familial ALS. | Q48838979 | ||
| Changes in excitability and impulse transmission following prolonged repetitive activity in normal subjects and patients with a focal nerve lesion | Q48840073 | ||
| Cortical hyperexcitability may precede the onset of familial amyotrophic lateral sclerosis | Q48881997 | ||
| Mutation in the Na+ channel subunit SCN1B produces paradoxical changes in peripheral nerve excitability | Q48951413 | ||
| Neuroprotection through excitability and mTOR required in ALS motoneurons to delay disease and extend survival | Q48957960 | ||
| Abnormalities of axonal excitability are not generalized in early multifocal motor neuropathy | Q49010012 | ||
| Strength-duration properties of human peripheral nerve | Q49022198 | ||
| Changes in excitability and accommodation of human motor axons following brief periods of ischaemia | Q50796248 | ||
| Evidence for two types of potassium channel in human motor axons in vivo | Q50800637 | ||
| Abnormal gating of axonal slow potassium current in cramp-fasciculation syndrome | Q51026606 | ||
| Function and distribution of three types of rectifying channel in rat spinal root myelinated axons | Q51795801 | ||
| Ischaemic changes in refractoriness of human cutaneous afferents under threshold-clamp conditions. | Q52170053 | ||
| Changes in excitability indices of cutaneous afferents produced by ischaemia in human subjects | Q52211540 | ||
| The strength-duration relationship for excitation of myelinated nerve: computed dependence on membrane parameters | Q52703872 | ||
| Modulatory effects on axonal function after intravenous immunoglobulin therapy in chronic inflammatory demyelinating polyneuropathy | Q53415914 | ||
| Heterogeneous distribution of fast and slow potassium channels in myelinated rat nerve fibres | Q54105891 | ||
| Electrical properties of isolated demyelinated rat nerve fibres | Q54529909 | ||
| The "split hand syndrome". | Q55033486 | ||
| Amyotrophic lateral sclerosis | Q55877676 | ||
| Characteristics of fasciculations in amyotrophic lateral sclerosis and the benign fasciculation syndrome | Q56531752 | ||
| Distal motor axonal dysfunction in amyotrophic lateral sclerosis | Q56771891 | ||
| Markedly reduced axonal potassium channel expression in human sporadic amyotrophic lateral sclerosis: An immunohistochemical study | Q56771914 | ||
| Changes in Na+ channel expression and nodal persistent Na+ currents associated with peripheral nerve regeneration in mice | Q56772056 | ||
| Distal excitability changes in motor axons in amyotrophic lateral sclerosis | Q56772179 | ||
| Increased nodal persistent Na+ currents in human neuropathy and motor neuron disease estimated by latent addition | Q56772190 | ||
| Threshold electrotonus in chronic inflammatory demyelinating polyneuropathy: Correlation with clinical profiles | Q56772255 | ||
| Cramps, muscle pain, and fasciculations: not always benign? | Q56929777 | ||
| Abnormal axonal inward rectification in diabetic neuropathy | Q59591788 | ||
| Increased expression of the beta3 subunit of voltage-gated Na+ channels in the spinal cord of the SOD1G93A mouse | Q61051663 | ||
| The origin of fasciculations | Q70558946 | ||
| Dose-ranging study of riluzole in amyotrophic lateral sclerosis. Amyotrophic Lateral Sclerosis/Riluzole Study Group II | Q71177245 | ||
| The effect of stimulus duration on the latency of submaximal nerve volleys | Q71535948 | ||
| Axonal ion channel dysfunction in amyotrophic lateral sclerosis | Q71681845 | ||
| Ion channels in human axons | Q72103168 | ||
| Intracellular recording from vertebrate myelinated axons: mechanism of the depolarizing afterpotential | Q72111004 | ||
| A controlled trial of riluzole in amyotrophic lateral sclerosis. ALS/Riluzole Study Group | Q72759362 | ||
| Neurotonia: Impulse-induced repetitive discharges in motor nerves in peripheral neuropathy | Q72867178 | ||
| Riluzole inhibits the persistent sodium current in mammalian CNS neurons | Q73072440 | ||
| Effects of membrane polarization and ischaemia on the excitability properties of human motor axons | Q73251210 | ||
| Complex fasciculations and their origin in amyotrophic lateral sclerosis and Kennedy's disease | Q73259817 | ||
| Excitability changes in human sensory and motor axons during hyperventilation and ischaemia | Q73264157 | ||
| Multiple measures of axonal excitability: a new approach in clinical testing | Q73459448 | ||
| Effects of temperature on the excitability properties of human motor axons | Q73711764 | ||
| Clinical evaluation of excitability measures in sensory nerve | Q74035734 | ||
| Activity‐dependent hyperpolarization of human motor axons produced by natural activity | Q74332016 | ||
| The use of botulinum toxin in localizing neuromyotonia to the terminal branches of the peripheral nerve | Q74509703 | ||
| Expression of X-linked bulbospinal muscular atrophy (Kennedy disease) in two homozygous women | Q74764200 | ||
| Modeling the excitability of mammalian nerve fibers: influence of afterpotentials on the recovery cycle | Q77590693 | ||
| Strength-duration properties of peripheral nerve in acquired neuromyotonia | Q77976814 | ||
| Strength-duration properties and their voltage dependence at different sites along the median nerve | Q78231214 | ||
| Global loss of Na,K-ATPase and its nitric oxide-mediated regulation in a transgenic mouse model of amyotrophic lateral sclerosis | Q78753171 | ||
| Sodium channel blockers as neuroprotectants in neuroinflammatory disease: a double-edged sword | Q80696272 | ||
| Multifocal motor neuropathy: decrease in conduction blocks and reinnervation with long-term IVIg | Q80847191 | ||
| Pathophysiologic insights into motor axonal function in Kennedy disease | Q81555835 | ||
| Nerve excitability changes after intravenous immunoglobulin infusions in multifocal motor neuropathy and chronic inflammatory demyelinating neuropathy | Q83169211 | ||
| Utility of recovery cycle with two conditioning pulses for detection of impaired axonal slow potassium current in ALS | Q84385694 | ||
| Progressive axonal dysfunction and clinical impairment in amyotrophic lateral sclerosis | Q84868234 | ||
| Adult spinal motoneurones are not hyperexcitable in a mouse model of inherited amyotrophic lateral sclerosis | Q87132998 | ||
| Multifocal motor neuropathy | Q87229413 | ||
| Chronic inflammatory demyelinating polyradiculoneuropathy: from pathology to phenotype | Q36005389 | ||
| Controversies and priorities in amyotrophic lateral sclerosis | Q36045826 | ||
| General mechanisms of axonal damage and its prevention | Q36130539 | ||
| Fatigue and activity dependent changes in axonal excitability in amyotrophic lateral sclerosis | Q36226795 | ||
| Abnormalities in cortical and peripheral excitability in flail arm variant amyotrophic lateral sclerosis | Q36227125 | ||
| A voltage-dependent persistent sodium current in mammalian hippocampal neurons | Q36410578 | ||
| Flecainide in Amyotrophic Lateral Sclerosis as a Neuroprotective Strategy (FANS): A Randomized Placebo-Controlled Trial. | Q36437641 | ||
| Axonal conduction and injury in multiple sclerosis: the role of sodium channels | Q36657811 | ||
| SMN deficiency causes tissue-specific perturbations in the repertoire of snRNAs and widespread defects in splicing | Q36746476 | ||
| A randomized trial of mexiletine in ALS: Safety and effects on muscle cramps and progression | Q36813236 | ||
| Mutant SOD1-expressing astrocytes release toxic factors that trigger motoneuron death by inducing hyperexcitability | Q36924065 | ||
| A SYNDROME OF CONTINUOUS MUSCLE-FIBRE ACTIVITY | Q37111804 | ||
| Neonatal neuronal circuitry shows hyperexcitable disturbance in a mouse model of the adult-onset neurodegenerative disease amyotrophic lateral sclerosis | Q37352278 | ||
| Axonal ion channels from bench to bedside: a translational neuroscience perspective | Q37584672 | ||
| Pathogenesis and therapy of spinal and bulbar muscular atrophy (SBMA). | Q38011490 | ||
| Advances in treating amyotrophic lateral sclerosis: insights from pathophysiological studies | Q38220095 | ||
| Intrinsic membrane hyperexcitability of amyotrophic lateral sclerosis patient-derived motor neurons | Q39007648 | ||
| A single blind randomized controlled clinical trial of mexiletine in amyotrophic lateral sclerosis: Efficacy and safety of sodium channel blocker phase II trial. | Q39008917 | ||
| Muscle cramp in Machado-Joseph disease: altered motor axonal excitability properties and mexiletine treatment | Q39397393 | ||
| 4-Aminopyridine Induced Activity Rescues Hypoexcitable Motor Neurons from Amyotrophic Lateral Sclerosis Patient-Derived Induced Pluripotent Stem Cells | Q39945217 | ||
| Hyperexcitability of motor and sensory neurons in neuromyotonia | Q40250103 | ||
| Altered axonal excitability properties in amyotrophic lateral sclerosis: impaired potassium channel function related to disease stage | Q40351989 | ||
| Increased HCN channel driven inward rectification in benign cramp fasciculation syndrome. | Q40571096 | ||
| The origin of muscle fasciculations and cramps | Q40637301 | ||
| Aberrant association of misfolded SOD1 with Na(+)/K(+)ATPase-α3 impairs its activity and contributes to motor neuron vulnerability in ALS. | Q41087321 | ||
| Queer current and pacemaker: the hyperpolarization-activated cation current in neurons | Q41117697 | ||
| Persistent sodium current in mammalian central neurons | Q41117708 | ||
| Threshold tracking techniques in the study of human peripheral nerve | Q41702491 | ||
| Early intrinsic hyperexcitability does not contribute to motoneuron degeneration in amyotrophic lateral sclerosis. | Q41957945 | ||
| Increased persistent sodium current determines cortical hyperexcitability in a genetic model of amyotrophic lateral sclerosis | Q42605747 | ||
| Cortical excitability in hereditary motor neuronopathy with pyramidal signs: comparison with ALS. | Q43216720 | ||
| The voltage dependence of I(h) in human myelinated axons | Q43494068 | ||
| Links between Electrophysiological and Molecular Pathology of Amyotrophic Lateral Sclerosis | Q43577107 | ||
| Split-hand index for the diagnosis of amyotrophic lateral sclerosis | Q43698165 | ||
| Pathophysiological insights derived by natural history and motor function of spinal muscular atrophy | Q43847282 | ||
| Nerve excitability changes in chronic renal failure indicate membrane depolarization due to hyperkalaemia | Q44002213 | ||
| ALS pathophysiology: insights from the split-hand phenomenon | Q44729991 | ||
| The syndrome of continuous muscle fiber activity. Evidence to suggest proximal neurogenic causation | Q45008869 | ||
| Motor axonal excitability properties are strong predictors for survival in amyotrophic lateral sclerosis | Q45063048 | ||
| Split hand syndrome in amyotrophic lateral sclerosis: different excitability changes in the thenar and hypothenar motor axons | Q45148790 | ||
| Increased persistent Na(+) current and its effect on excitability in motoneurones cultured from mutant SOD1 mice. | Q45223589 | ||
| Clinical and electrodiagnostic features of X-linked recessive bulbospinal neuronopathy | Q46503839 | ||
| Altered motor nerve excitability in end-stage kidney disease | Q46537689 | ||
| P433 | issue | 1 | |
| P921 | main subject | amyotrophic lateral sclerosis | Q206901 |
| P304 | page(s) | 78-90 | |
| P577 | publication date | 2016-11-22 | |
| P13046 | publication type of scholarly work | review article | Q7318358 |
| P1433 | published in | Neurotherapeutics | Q15716631 |
| P1476 | title | Axonal Excitability in Amyotrophic Lateral Sclerosis : Axonal Excitability in ALS. | |
| P478 | volume | 14 |
| Q88409196 | Acute Effects of Riluzole and Retigabine on Axonal Excitability in Patients With Amyotrophic Lateral Sclerosis: A Randomized, Double-Blind, Placebo-Controlled, Crossover Trial |
| Q49892100 | An Appraisal of Novel Biomarkers for Evaluating and Monitoring Neurologic Diseases: Editorial Introduction |
| Q64079969 | Biomarkers in Motor Neuron Disease: A State of the Art Review |
| Q88599808 | Functional up-regulation of the M-current by retigabine contrasts hyperexcitability and excitotoxicity on rat hypoglossal motoneurons |
| Q92883641 | Genetic T-type calcium channelopathies |
| Q59591786 | In vivo evidence for reduced ion channel expression in motor axons of patients with amyotrophic lateral sclerosis |
| Q51139700 | Ingestion of transient receptor potential channel agonists attenuates exercise-induced muscle cramps |
| Q92103711 | Ion channel dysfunction and altered motoneuron excitability in ALS |
| Q57170405 | Ionic Homeostasis Maintenance in ALS: Focus on New Therapeutic Targets |
| Q64917154 | Monozygotic twins and triplets discordant for amyotrophic lateral sclerosis display differential methylation and gene expression. |
| Q49905442 | Synaptic dysfunction and altered excitability in C9ORF72 ALS/FTD. |
| Q91781195 | The Peripheral Nervous System in Amyotrophic Lateral Sclerosis: Opportunities for Translational Research |
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