| scholarly article | Q13442814 |
| P50 | author | Shamima Rahman | Q88384447 |
| P2093 | author name string | Simon J R Heales | |
| Elisa Fassone | |||
| Marta Kanabus | |||
| Maura O' Donnell | |||
| Sara Farahi Bilooei | |||
| Sean David Hughes | |||
| Tricia Rutherford | |||
| P2860 | cites work | Cochrane Database of Systematic Reviews | Q15750361 |
| Diagnostic criteria for respiratory chain disorders in adults and children. | Q51697654 | ||
| Biomarkers of mitochondrial content in skeletal muscle of healthy young human subjects | Q58456009 | ||
| Early-Onset Ophthalmoplegia in Leigh-Like Syndrome Due to NDUFV1 Mutations | Q63681411 | ||
| Effects of valproate on biogenesis and function of liver mitochondria | Q70129578 | ||
| Monitoring octanoic and decanoic acids in plasma from children with intractable epilepsy treated with medium-chain triglyceride diet | Q70333792 | ||
| Mitochondrial damage: an important feature in a number of inborn errors of metabolism? | Q71345278 | ||
| Valproate and cytochrome c oxidase deficiency | Q72643297 | ||
| Effect of bezafibrate treatment on late-onset mitochondrial myopathy in mice | Q82107861 | ||
| Treatment for mitochondrial disorders | Q24200432 | ||
| Subacute necrotizing encephalomyelopathy in an infant | Q24564004 | ||
| Identification and Mechanism of 10-Carbon Fatty Acid as Modulating Ligand of Peroxisome Proliferator-activated Receptors | Q27675297 | ||
| The ketogenic diet component decanoic acid increases mitochondrial citrate synthase and complex I activity in neuronal cells | Q28304995 | ||
| Screening for active small molecules in mitochondrial complex I deficient patient's fibroblasts, reveals AICAR as the most beneficial compound | Q28477645 | ||
| The kinetic properties of citrate synthase from rat liver mitochondria | Q28570044 | ||
| High protonic potential actuates a mechanism of production of reactive oxygen species in mitochondria | Q28610852 | ||
| Mitochondrial glutathione, a key survival antioxidant | Q33649876 | ||
| Risk of acute myocardial infarction, stroke, heart failure, and death in elderly Medicare patients treated with rosiglitazone or pioglitazone | Q34123137 | ||
| Ketogenic treatment reduces deleted mitochondrial DNAs in cultured human cells | Q34351534 | ||
| Mitochondrial biogenesis in the anticonvulsant mechanism of the ketogenic diet | Q34542879 | ||
| Ketogenic diet, brain glutamate metabolism and seizure control | Q35652460 | ||
| Mitochondrial disorders: prevalence, myths and advances. | Q35800518 | ||
| Development of pharmacological strategies for mitochondrial disorders | Q37686237 | ||
| Mitochondrial disease and epilepsy | Q37979255 | ||
| Complex I deficiency: clinical features, biochemistry and molecular genetics | Q38042908 | ||
| Gastrointestinal and hepatic manifestations of mitochondrial disorders | Q38106894 | ||
| Leigh syndrome: One disorder, more than 75 monogenic causes | Q38617364 | ||
| AMPK: An Energy-Sensing Pathway with Multiple Inputs and Outputs | Q38652124 | ||
| Human neuronal coenzyme Q10 deficiency results in global loss of mitochondrial respiratory chain activity, increased mitochondrial oxidative stress and reversal of ATP synthase activity: implications for pathogenesis and treatment. | Q39318947 | ||
| PPAR-gamma: adipogenic regulator and thiazolidinedione receptor | Q41755813 | ||
| Ketogenic diet slows down mitochondrial myopathy progression in mice | Q43157369 | ||
| A randomized trial of classical and medium-chain triglyceride ketogenic diets in the treatment of childhood epilepsy | Q44147677 | ||
| Polyunsaturated fatty acid-enriched diet therapy for a child with epilepsy. | Q45735701 | ||
| The ketogenic diet increases mitochondrial glutathione levels. | Q46605111 | ||
| Induction of mitochondrial oxidative stress in astrocytes by nitric oxide precedes disruption of energy metabolism | Q46653962 | ||
| The ketogenic diet increases mitochondrial uncoupling protein levels and activity | Q47866548 | ||
| Energy thresholds in brain mitochondria. Potential involvement in neurodegeneration. | Q48462986 | ||
| Landau-Kleffner syndrome with mitochondrial respiratory chain-complex I deficiency. | Q48494343 | ||
| A case of Ohtahara syndrome with mitochondrial respiratory chain complex I deficiency | Q48733444 | ||
| Leigh syndrome: clinical features and biochemical and DNA abnormalities. | Q49107059 | ||
| P275 | copyright license | Creative Commons Attribution 4.0 International | Q20007257 |
| P6216 | copyright status | copyrighted | Q50423863 |
| P433 | issue | 3 | |
| P921 | main subject | pleiotropy | Q1134884 |
| P304 | page(s) | 415-426 | |
| P577 | publication date | 2016-04-14 | |
| P1433 | published in | Journal of Inherited Metabolic Disease | Q6295359 |
| P1476 | title | The pleiotropic effects of decanoic acid treatment on mitochondrial function in fibroblasts from patients with complex I deficient Leigh syndrome | |
| P478 | volume | 39 |
| Q91068984 | Advances in the treatment of mitochondrial epilepsies |
| Q38859815 | An examination of biochemical parameters and their association with response to ketogenic dietary therapies |
| Q89910241 | Dietary α-cyclodextrin reduces atherosclerosis and modifies gut flora in apolipoprotein E-deficient mice |
| Q90010105 | Functional Consequences of PDK4 Deficiency in Doberman Pinscher Fibroblasts |
| Q91813202 | Ketogenic diet regulates the antioxidant catalase via the transcription factor PPARγ2 |
| Q47771228 | Mechanisms of action for the medium-chain triglyceride ketogenic diet in neurological and metabolic disorders. |
| Q41840468 | Metabolic flexibility of mitochondrial respiratory chain disorders predicted by computer modelling |
| Q89106395 | Mitochondrial medicine in the omics era |
| Q38697952 | Neuronal decanoic acid oxidation is markedly lower than that of octanoic acid: A mechanistic insight into the medium-chain triglyceride ketogenic diet |
| Q39111856 | New insights into the mechanisms of the ketogenic diet. |
| Q46273409 | Oxidative Stress: Mechanistic Insights into Inherited Mitochondrial Disorders and Parkinson's Disease |
| Q93209103 | POLG-related disorders and their neurological manifestations |
| Q43106711 | Selection and Characterization of Palmitic Acid Responsive Patients with an OXPHOS Complex I Defect |
Search more.