| scholarly article | Q13442814 |
| P2093 | author name string | Sorin V Fedeles | |
| Stefan Somlo | |||
| Seung Hun Lee | |||
| Ann-Hwee Lee | |||
| Jae-Seon So | |||
| Anna-Rachel Gallagher | |||
| Christina E Barkauskas | |||
| Amol Shrikhande | |||
| P2860 | cites work | XBP1 links ER stress to intestinal inflammation and confers genetic risk for human inflammatory bowel disease | Q22252318 |
| Cleavage of polycystin-1 requires the receptor for egg jelly domain and is disrupted by human autosomal-dominant polycystic kidney disease 1-associated mutations. | Q24336734 | ||
| Mutations in PRKCSH cause isolated autosomal dominant polycystic liver disease | Q24531988 | ||
| A novel evolutionarily conserved domain of cell-adhesion GPCRs mediates autoproteolysis | Q24602445 | ||
| Getting in and out from calnexin/calreticulin cycles | Q24646392 | ||
| Cre reporter strains produced by targeted insertion of EYFP and ECFP into the ROSA26 locus | Q24797230 | ||
| Polycystin-1: a master regulator of intersecting cystic pathways | Q26826955 | ||
| Targeted mutation of the mouse Grp94 gene disrupts development and perturbs endoplasmic reticulum stress signaling | Q27326154 | ||
| Sec63p and Kar2p are required for the translocation of SRP-dependent precursors into the yeast endoplasmic reticulum in vivo | Q27930764 | ||
| BiP acts as a molecular ratchet during posttranslational transport of prepro-alpha factor across the ER membrane | Q27932673 | ||
| BiP and Sec63p are required for both co- and posttranslational protein translocation into the yeast endoplasmic reticulum | Q27935171 | ||
| Proteasome inhibitors disrupt the unfolded protein response in myeloma cells | Q28155919 | ||
| Germline mutations in PRKCSH are associated with autosomal dominant polycystic liver disease | Q28208353 | ||
| Unfolded proteins are Ire1-activating ligands that directly induce the unfolded protein response | Q38845249 | ||
| The cotranslational maturation of the type I membrane glycoprotein tyrosinase: the heat shock protein 70 system hands off to the lectin-based chaperone system | Q40409191 | ||
| Clinical profile of autosomal dominant polycystic liver disease | Q44261201 | ||
| Sec61p and BiP directly facilitate polypeptide translocation into the ER. | Q45975576 | ||
| The molecular basis of focal cyst formation in human autosomal dominant polycystic kidney disease type I. | Q48056738 | ||
| Somatic mutation in individual liver cysts supports a two-hit model of cystogenesis in autosomal dominant polycystic kidney disease. | Q55067904 | ||
| Polycystic liver disease | Q70962844 | ||
| Somatic inactivation of Pkd2 results in polycystic kidney disease | Q74502174 | ||
| Protein transport into the endoplasmic reticulum: mechanisms and pathologies | Q79312755 | ||
| Activation of myeloid cell-specific adhesion class G protein-coupled receptor EMR2 via ligation-induced translocation and interaction of receptor subunits in lipid raft microdomains | Q28259067 | ||
| Mutations in SEC63 cause autosomal dominant polycystic liver disease | Q28260838 | ||
| GPS autoproteolysis is required for CD97 to up-regulate the expression of N-cadherin that promotes homotypic cell-cell aggregation | Q28300855 | ||
| Plasma cell differentiation and the unfolded protein response intersect at the transcription factor XBP-1 | Q28507338 | ||
| Regulation of hepatic lipogenesis by the transcription factor XBP1 | Q28507784 | ||
| XBP-1 Regulates a Subset of Endoplasmic Reticulum Resident Chaperone Genes in the Unfolded Protein Response | Q28585314 | ||
| Polycystin-2 localizes to kidney cilia and the ciliary level is elevated in orpk mice with polycystic kidney disease | Q28585961 | ||
| ERdj4 protein is a soluble endoplasmic reticulum (ER) DnaJ family protein that interacts with ER-associated degradation machinery | Q28587463 | ||
| A genetic interaction network of five genes for human polycystic kidney and liver diseases defines polycystin-1 as the central determinant of cyst formation | Q28590393 | ||
| ER stress regulation of ATF6 localization by dissociation of BiP/GRP78 binding and unmasking of Golgi localization signals | Q28646129 | ||
| Dynamic interaction of BiP and ER stress transducers in the unfolded-protein response | Q29547299 | ||
| The unfolded protein response: from stress pathway to homeostatic regulation | Q29547396 | ||
| The HSP70 chaperone machinery: J proteins as drivers of functional specificity | Q29616140 | ||
| Polycystic kidney disease | Q33709685 | ||
| Stable binding of ATF6 to BiP in the endoplasmic reticulum stress response | Q33713564 | ||
| J domain co-chaperone specificity defines the role of BiP during protein translocation | Q33991043 | ||
| Secondary, somatic mutations might promote cyst formation in patients with autosomal dominant polycystic liver disease. | Q33998303 | ||
| Identification and characterization of a novel endoplasmic reticulum (ER) DnaJ homologue, which stimulates ATPase activity of BiP in vitro and is induced by ER stress | Q34113413 | ||
| XBP1, downstream of Blimp-1, expands the secretory apparatus and other organelles, and increases protein synthesis in plasma cell differentiation | Q34345459 | ||
| Loss of heterozygosity is present in SEC63 germline carriers with polycystic liver disease | Q34500168 | ||
| Retro-translocation of proteins from the endoplasmic reticulum into the cytosol | Q34627241 | ||
| Altered trafficking and stability of polycystins underlie polycystic kidney disease | Q35145360 | ||
| Homologs of the yeast Sec complex subunits Sec62p and Sec63p are abundant proteins in dog pancreas microsomes | Q35155249 | ||
| IRE1α activation protects mice against acetaminophen-induced hepatotoxicity | Q35760821 | ||
| Essential role of cleavage of Polycystin-1 at G protein-coupled receptor proteolytic site for kidney tubular structure. | Q36276959 | ||
| Endoplasmic reticulum stress sensing in the unfolded protein response | Q36626672 | ||
| Syntaxin 5 regulates the endoplasmic reticulum channel-release properties of polycystin-2. | Q36948959 | ||
| The endoplasmic reticulum stress response in immunity and autoimmunity | Q37231726 | ||
| Glucosidase II beta subunit modulates N-glycan trimming in fission yeasts and mammals | Q37327323 | ||
| Direct derivation of conditionally immortal cell lines from an H-2Kb-tsA58 transgenic mouse | Q37530481 | ||
| Life and death of a BiP substrate | Q37660656 | ||
| GPS proteolytic cleavage of adhesion-GPCRs | Q37880762 | ||
| Identification and characterization of polycystin-2, the PKD2 gene product | Q38320261 | ||
| Interaction of BiP with the J-domain of the Sec63p component of the endoplasmic reticulum protein translocation complex. | Q38322966 | ||
| BiP and immunoglobulin light chain cooperate to control the folding of heavy chain and ensure the fidelity of immunoglobulin assembly | Q38612305 | ||
| P433 | issue | 5 | |
| P407 | language of work or name | English | Q1860 |
| P304 | page(s) | 1955-1967 | |
| P577 | publication date | 2015-04-06 | |
| P1433 | published in | Journal of Clinical Investigation | Q3186904 |
| P1476 | title | Sec63 and Xbp1 regulate IRE1α activity and polycystic disease severity | |
| P478 | volume | 125 |
| Q91473818 | Effective reconstruction of functional organotypic kidney spheroid for in vitro nephrotoxicity studies |
| Q36746091 | Essential Role of X-Box Binding Protein-1 during Endoplasmic Reticulum Stress in Podocytes. |
| Q47133560 | Inhibition of IRE1α-mediated XBP1 mRNA cleavage by XBP1 reveals a novel regulatory process during the unfolded protein response. |
| Q38708994 | Isolated polycystic liver disease genes define effectors of polycystin-1 function |
| Q36355151 | Mutant uromodulin expression leads to altered homeostasis of the endoplasmic reticulum and activates the unfolded protein response. |
| Q34529587 | Mutations in GANAB, Encoding the Glucosidase IIα Subunit, Cause Autosomal-Dominant Polycystic Kidney and Liver Disease |
| Q52372960 | Pharmacological targeting of MYC-regulated IRE1/XBP1 pathway suppresses MYC-driven breast cancer. |
| Q94519328 | Polycystic kidney disease |
| Q90636660 | Renal tubular cell spliced X-box binding protein 1 (Xbp1s) has a unique role in sepsis-induced acute kidney injury and inflammation |
| Q38754935 | Role of apoptosis in the development of autosomal dominant polycystic kidney disease (ADPKD). |
| Q92025214 | The cellular prion protein is a stress protein secreted by renal tubular cells and a urinary marker of kidney injury |
| Q64916381 | The endoplasmic reticulum (ER) chaperone BiP is a master regulator of ER functions: Getting by with a little help from ERdj friends. |
| Q49360155 | Urinary Angiogenin Reflects the Magnitude of Kidney Injury at the Infrahistologic Level |
| Q36651027 | mTORC1-mediated inhibition of polycystin-1 expression drives renal cyst formation in tuberous sclerosis complex |
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